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- W2058774552 abstract "A ceratodermia hereditária mutilante ou síndrome de Vohwinkel é afecção dermatológica rara caracterizada pelo espessamento cutâneo das palmas, plantas e dorso de mãos e pés, e por constrições em faixa dos dedos (pseudoainhum). São relatados três casos em uma família, envolvendo duas gerações. Em todos havia, adicionalmente, perda auditiva neurossensorial. Discutem-se o diagnóstico diferencial com outras ceratodermias palmoplantares e o tratamento com retinóides. Trata-se da primeira descrição dessa entidade no Brasil." @default.
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- W2058774552 date "2003-06-01" @default.
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- W2058774552 title "Ceratodermia mutilante de Vohwinkel: relato de três casos em uma família" @default.
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- W2058774552 doi "https://doi.org/10.1590/s0365-05962003000300007" @default.
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