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- W2065203574 abstract "Desmoid tumors are rare, benign, fibromatous lesions that are the result of abnormal proliferation of myofibroblasts. Desmoid tumors can be classified as extra-abdominal and abdominal. Abdominal desmoid tumors are either superficial or intraabdominal. These tumors are associated with a high recurrence rates, even if their microscopic characters indicate a benign disease; their biologic behavior often indicates rather a “malignant” disease, which can cause even the death. Intraabdominal desmoid tumors can engulf surrounding viscera and vessels, thereby greatly complicating their surgical treatment. Management is multidisciplinary. Simple observation is a reasonable management option for asymptomatic patients; spontaneous regression of these tumors may be observed. Complete excision is the treatment of choice for tumors causing symptoms or complications. Surgery should be minimized as much as feasible, while at the same time achieving free margins. Adjuvant therapy should be considered in selected cases; the role of other management options (including gene transfer therapy) is currently under intensive investigation." @default.
- W2065203574 created "2016-06-24" @default.
- W2065203574 creator A5049840505 @default.
- W2065203574 creator A5085341495 @default.
- W2065203574 creator A5085354540 @default.
- W2065203574 date "2007-08-01" @default.
- W2065203574 modified "2023-10-17" @default.
- W2065203574 title "Abdominal desmoid tumors" @default.
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- W2065203574 doi "https://doi.org/10.1016/j.suronc.2007.07.009" @default.
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