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- W2068128974 abstract "Les micropapules blanchâtres du visage du nouveau-né sont fréquentes et le plus souvent secondaires à une hyperplasie sébacée. Dans d’autres cas, elles correspondent à des grains de milium. L’abondance de ces derniers doit faire évoquer des diagnostics rares. Nous rapportons le cas d’un enfant présentant une éruption congénitale profuse de grains de milium du visage, spontanément résolutive. Cette éruption s’intègre dans le cadre du syndrome de Basan, génodermatose de transmission autosomique dominante qui associe grains de milium profus congénitaux du visage, bulles acrales, absence de dermatoglyphes et hyposudation palmoplantaire. White micropapules are uncommon on the face newborns and are mainly due to sebaceous hyperplasia, or more rarely to milia. In some cases they may result from milia and profuse milia suggest rare diseases. We report the case of a newborn presenting with profuse congenital milia on the face that resolved spontaneously within a few months. This eruption revealed Basan's syndrome, a rare, autosomal dominant inherited dermatosis described as the association of profuse facial milia, acral bullae, absence of dermatoglyphs, and palmoplantar hypohydrosis." @default.
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- W2068128974 date "2009-05-01" @default.
- W2068128974 modified "2023-09-27" @default.
- W2068128974 title "Absence de dermatoglyphes et grains de milium congénitaux : un nouveau cas de syndrome de Basan" @default.
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- W2068128974 doi "https://doi.org/10.1016/j.annder.2008.09.018" @default.
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