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- W2068667143 abstract "Resumo A fibrose quistica (FQ) e a doenca autossomica recessiva mais frequente na raca caucasiana. Caracteriza-se por mutacoes na CFTR, uma proteina transmembranar responsavel pelo transporte de cloretos. Esta proteina tem uma ampla distribuicao epitelial, o que da um caracter sistemico a esta doenca e consequentemente multiplas manifestacoes clinicas de gravidade variavel. A melhoria dos cuidados de saude, associada ao desenvolvimento do arsenal terapeutico, permitiu um aumento da sobrevida destes doentes, de tal forma que a FQ ja nao pode ser abordada como doenca da idade pediatrica. Tambem a evolucao tecnica na transplantacao abriu novas perspectivas quanto ao tratamento desta afeccao. Assim, cada vez mais esta patologia implica um envolvimento multidisciplinar no qual a pneumologia tem uma parte preponderante." @default.
- W2068667143 created "2016-06-24" @default.
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- W2068667143 date "2008-01-01" @default.
- W2068667143 modified "2023-10-02" @default.
- W2068667143 title "Fibrose quística: Revisão" @default.
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