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- W2069813052 abstract "Nous rapportons deux cas pédiatriques de thrombose de la veine cave supérieure diagnostiqués lors de la prise en charge d’un lymphome B primitif du médiastin (PMBCL). Le PMBCL est rare chez l’enfant et l’adolescent et aucun cas, à notre connaissance, de thrombose n’a été décrit dans cette situation. Les thromboses compliquant les lymphomes sont fréquemment asymptomatiques, découvertes fortuitement dans les premiers mois suivant le diagnostic. La physiopathologie est multifactorielle : compression veineuse par la masse, risque accru de thromboses dans les néoplasies, présence d’un cathéter central. Les principaux facteurs de risque rapportés dans la littérature sont : le haut grade du lymphome, l’existence de comorbidités, un envahissement neuro-méningé et une atteinte médiastinale. Les thromboses veineuses profondes (TVP) pouvant modifier le pronostic et la prise en charge des PMBCL, il est important de mieux connaître leurs facteurs de risque afin de mieux les dépister ou de les prévenir.We report two pediatric cases of superior vena cava thrombosis (VTE) in patients treated for primary mediastinal large B-cell lymphoma (PMBCL). PMBCL is a rare entity in children and adolescents and no thrombosis has been described in this population. Thrombosis in lymphoma is frequently asymptomatic, detected as an incidental finding in the first months following diagnosis. The thrombosis mechanisms are often multifactorial based on veinous compression by the mass, elevated risk of thrombosis in neoplasia, and/or presence of a central catheter. The risk factors of venous thromboembolism (VTE) in lymphoma are high-grade lymphoma, comorbidities, central nervous system lymphoma, and mediastinal mass. Because thrombosis has an impact on prognosis and treatment, it seems important to improve knowledge in order to improve the diagnosis and prevention of thrombosis in lymphoma." @default.
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- W2069813052 date "2011-06-01" @default.
- W2069813052 modified "2023-10-18" @default.
- W2069813052 title "Hypothermie périodique spontanée : à propos d’un cas traité efficacement par Keppra" @default.
- W2069813052 doi "https://doi.org/10.1016/j.revmed.2011.03.233" @default.
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