Matches in SemOpenAlex for { <https://semopenalex.org/work/W2076150806> ?p ?o ?g. }
Showing items 1 to 83 of
83
with 100 items per page.
- W2076150806 endingPage "25319" @default.
- W2076150806 startingPage "25319" @default.
- W2076150806 abstract "Myotonic dystrophy (DM) is an inherited progressive muscle disorder caused by defects in muscle proteins. As the incidence of this condition is low, not many are familiar with the multisystem involvement. At times, cardiac disease may even be the predominant manifestation in the form of arrhythmias, conduction defects, and cardiomyopathies. The progression of the disease can lead to sudden, unpredictable death. Thus, it is important to identify this subgroup and treat accordingly.To identify patients with DM and assess their risk for sudden cardiac death.Nine patients previously diagnosed with muscular dystrophy were evaluated by cardiologists for various reasons, from a general follow-up to cardiac arrest. All of them had electrocardiograms (EKG) and 2-D echocardiograms, and seven of them had further electrophysiological (EP) studies.Of the nine patients with DM, eight had EKG evidence of conduction abnormalities ranging from first-degree heart block to complete heart block. Of the seven who had EP studies, five had inducible ventricular tachycardia requiring immediate cardioversion and implantable cardioverter defibrillator (ICD) implant. Two of them underwent permanent pacemaker placement due to complete heart block and infra-Hissian block. The remaining two patients opted for a conservative approach with yearly EKG monitoring.Because one-third of the cardiac deaths in patients with DM are sudden, there is a strong need to identify these patients and intervene in those at high risk. Prophylactic pacemaker placement is recommended even in those with minimal conduction system abnormality. However, the common practice is to identify patients at high risk of conduction abnormalities by EP studies and then provide them with prophylactic invasive strategies." @default.
- W2076150806 created "2016-06-24" @default.
- W2076150806 creator A5000792891 @default.
- W2076150806 creator A5027465885 @default.
- W2076150806 creator A5036796506 @default.
- W2076150806 creator A5076898325 @default.
- W2076150806 date "2015-01-01" @default.
- W2076150806 modified "2023-09-23" @default.
- W2076150806 title "Cardiac involvement in myotonic dystrophy" @default.
- W2076150806 cites W1974128841 @default.
- W2076150806 cites W1975701091 @default.
- W2076150806 cites W2030464609 @default.
- W2076150806 cites W2042602665 @default.
- W2076150806 cites W2047560065 @default.
- W2076150806 cites W207415698 @default.
- W2076150806 cites W2083028245 @default.
- W2076150806 cites W2126428415 @default.
- W2076150806 cites W2143435617 @default.
- W2076150806 cites W2169743447 @default.
- W2076150806 cites W53181040 @default.
- W2076150806 doi "https://doi.org/10.3402/jchimp.v5.25319" @default.
- W2076150806 hasPubMedCentralId "https://www.ncbi.nlm.nih.gov/pmc/articles/4318833" @default.
- W2076150806 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/25656662" @default.
- W2076150806 hasPublicationYear "2015" @default.
- W2076150806 type Work @default.
- W2076150806 sameAs 2076150806 @default.
- W2076150806 citedByCount "4" @default.
- W2076150806 countsByYear W20761508062015 @default.
- W2076150806 countsByYear W20761508062016 @default.
- W2076150806 countsByYear W20761508062017 @default.
- W2076150806 countsByYear W20761508062021 @default.
- W2076150806 crossrefType "journal-article" @default.
- W2076150806 hasAuthorship W2076150806A5000792891 @default.
- W2076150806 hasAuthorship W2076150806A5027465885 @default.
- W2076150806 hasAuthorship W2076150806A5036796506 @default.
- W2076150806 hasAuthorship W2076150806A5076898325 @default.
- W2076150806 hasBestOaLocation W20761508061 @default.
- W2076150806 hasConcept C126322002 @default.
- W2076150806 hasConcept C164705383 @default.
- W2076150806 hasConcept C2775935837 @default.
- W2076150806 hasConcept C2776331378 @default.
- W2076150806 hasConcept C2776661526 @default.
- W2076150806 hasConcept C2777289489 @default.
- W2076150806 hasConcept C2778063965 @default.
- W2076150806 hasConcept C2779161974 @default.
- W2076150806 hasConcept C2780040984 @default.
- W2076150806 hasConcept C2993353509 @default.
- W2076150806 hasConcept C71924100 @default.
- W2076150806 hasConceptScore W2076150806C126322002 @default.
- W2076150806 hasConceptScore W2076150806C164705383 @default.
- W2076150806 hasConceptScore W2076150806C2775935837 @default.
- W2076150806 hasConceptScore W2076150806C2776331378 @default.
- W2076150806 hasConceptScore W2076150806C2776661526 @default.
- W2076150806 hasConceptScore W2076150806C2777289489 @default.
- W2076150806 hasConceptScore W2076150806C2778063965 @default.
- W2076150806 hasConceptScore W2076150806C2779161974 @default.
- W2076150806 hasConceptScore W2076150806C2780040984 @default.
- W2076150806 hasConceptScore W2076150806C2993353509 @default.
- W2076150806 hasConceptScore W2076150806C71924100 @default.
- W2076150806 hasIssue "1" @default.
- W2076150806 hasLocation W20761508061 @default.
- W2076150806 hasLocation W20761508062 @default.
- W2076150806 hasLocation W20761508063 @default.
- W2076150806 hasLocation W20761508064 @default.
- W2076150806 hasOpenAccess W2076150806 @default.
- W2076150806 hasPrimaryLocation W20761508061 @default.
- W2076150806 hasRelatedWork W2009378781 @default.
- W2076150806 hasRelatedWork W2063054225 @default.
- W2076150806 hasRelatedWork W2076150806 @default.
- W2076150806 hasRelatedWork W2158345876 @default.
- W2076150806 hasRelatedWork W2398206901 @default.
- W2076150806 hasRelatedWork W2413890202 @default.
- W2076150806 hasRelatedWork W2413952890 @default.
- W2076150806 hasRelatedWork W2474671174 @default.
- W2076150806 hasRelatedWork W3146409838 @default.
- W2076150806 hasRelatedWork W2083969769 @default.
- W2076150806 hasVolume "5" @default.
- W2076150806 isParatext "false" @default.
- W2076150806 isRetracted "false" @default.
- W2076150806 magId "2076150806" @default.
- W2076150806 workType "article" @default.