FRINK Linked Data Fragments server

Matches in SemOpenAlex for { <https://semopenalex.org/work/W2076168031> ?p ?o ?g. }

• W2076168031 endingPage "185" @default.
• W2076168031 startingPage "159" @default.
• W2076168031 abstract "Hereditary spongiform dystrophy in young children is characterised by macrocephaly with spasticity, convulsions and ultimately a decerebrate state and diffuse electro-encephalographic changes. Histological examination of the brain remains essential for its diagnosis. A review of the ultrastructural studies reported by various authors complements the findings obtained by conventional histology. We have thus endeavoured to determine whether van Bogaert-Bertrand's disease is to be considered as congenital or acquired. The anatomical findings in 3 cases together with the descriptions of other authors lead us to the following conclusions: &#x02022;- that the spongiform changes may be due to an osmolar disequilibrium in which the relation with mitochondrial abnormalities is yet unclear. &#x02022;- that the constant finding of Alzheimer type II cells is certainly an indication of intra-astrocytic malfunction. &#x02022;- that the oedema blocks both myelin synthesis and its coiling into lamellae. Case 1, which showed a long survival compared to others described (about 4 years), enabled us to study terminal lesions. Sub-cortical zones, in both cerebrum and cerebellum, contained neither myelin nor spongiform cavities, but, on the other hand, showed a compact glio-fibrillosis with large vesicles and oligodendroglia of increased density. We have interpreted these lesions, progressively replaced by spongiosis deeper in the cortex, as evidence of retracted scar tissue. Differences found between cerebral weights seem to confirm this hypothesis." @default.
• W2076168031 created "2016-06-24" @default.
• W2076168031 creator A5068402235 @default.
• W2076168031 date "1976-06-01" @default.
• W2076168031 modified "2023-09-25" @default.
• W2076168031 title "La dystrophie spongieuse hereditaire des enfants (Canavan: Van Bogaert-Bertrand)" @default.
• W2076168031 cites W152287780 @default.
• W2076168031 cites W1569125973 @default.
• W2076168031 cites W1966141736 @default.
• W2076168031 cites W1969678141 @default.
• W2076168031 cites W1973698599 @default.
• W2076168031 cites W1976704090 @default.
• W2076168031 cites W1982024245 @default.
• W2076168031 cites W1982091029 @default.
• W2076168031 cites W1994035768 @default.
• W2076168031 cites W1994313864 @default.
• W2076168031 cites W1998231632 @default.
• W2076168031 cites W2011341025 @default.
• W2076168031 cites W2013186925 @default.
• W2076168031 cites W2015983762 @default.
• W2076168031 cites W2016777902 @default.
• W2076168031 cites W2019345222 @default.
• W2076168031 cites W2019483307 @default.
• W2076168031 cites W2019776931 @default.
• W2076168031 cites W2025651098 @default.
• W2076168031 cites W2029385899 @default.
• W2076168031 cites W2044649270 @default.
• W2076168031 cites W2067859408 @default.
• W2076168031 cites W2084573446 @default.
• W2076168031 cites W2086780152 @default.
• W2076168031 cites W2090190597 @default.
• W2076168031 cites W2095406026 @default.
• W2076168031 cites W2142751194 @default.
• W2076168031 cites W2162315598 @default.
• W2076168031 cites W2164876881 @default.
• W2076168031 cites W2314338388 @default.
• W2076168031 cites W2315655718 @default.
• W2076168031 cites W2317747321 @default.
• W2076168031 cites W2319911740 @default.
• W2076168031 cites W2321407507 @default.
• W2076168031 cites W2322422069 @default.
• W2076168031 cites W2323218320 @default.
• W2076168031 cites W2325268474 @default.
• W2076168031 cites W2333923926 @default.
• W2076168031 cites W2335702356 @default.
• W2076168031 cites W2398435358 @default.
• W2076168031 cites W2400991030 @default.
• W2076168031 cites W2402772891 @default.
• W2076168031 cites W2434085137 @default.
• W2076168031 cites W2911893001 @default.
• W2076168031 cites W2912879501 @default.
• W2076168031 cites W2997063922 @default.
• W2076168031 cites W310193716 @default.
• W2076168031 cites W328213939 @default.
• W2076168031 cites W4293583508 @default.
• W2076168031 cites W52091884 @default.
• W2076168031 cites W2094929288 @default.
• W2076168031 cites W2328983497 @default.
• W2076168031 doi "https://doi.org/10.1016/0022-510x(76)90101-5" @default.
• W2076168031 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/1271080" @default.
• W2076168031 hasPublicationYear "1976" @default.
• W2076168031 type Work @default.
• W2076168031 sameAs 2076168031 @default.
• W2076168031 citedByCount "11" @default.
• W2076168031 countsByYear W20761680312015 @default.
• W2076168031 countsByYear W20761680312016 @default.
• W2076168031 countsByYear W20761680312018 @default.
• W2076168031 countsByYear W20761680312021 @default.
• W2076168031 crossrefType "journal-article" @default.
• W2076168031 hasAuthorship W2076168031A5068402235 @default.
• W2076168031 hasConcept C105702510 @default.
• W2076168031 hasConcept C142724271 @default.
• W2076168031 hasConcept C169760540 @default.
• W2076168031 hasConcept C2778609137 @default.
• W2076168031 hasConcept C2780182102 @default.
• W2076168031 hasConcept C529278444 @default.
• W2076168031 hasConcept C71924100 @default.
• W2076168031 hasConcept C86803240 @default.
• W2076168031 hasConceptScore W2076168031C105702510 @default.
• W2076168031 hasConceptScore W2076168031C142724271 @default.
• W2076168031 hasConceptScore W2076168031C169760540 @default.
• W2076168031 hasConceptScore W2076168031C2778609137 @default.
• W2076168031 hasConceptScore W2076168031C2780182102 @default.
• W2076168031 hasConceptScore W2076168031C529278444 @default.
• W2076168031 hasConceptScore W2076168031C71924100 @default.
• W2076168031 hasConceptScore W2076168031C86803240 @default.
• W2076168031 hasIssue "2" @default.
• W2076168031 hasLocation W20761680311 @default.
• W2076168031 hasLocation W20761680312 @default.
• W2076168031 hasOpenAccess W2076168031 @default.
• W2076168031 hasPrimaryLocation W20761680311 @default.
• W2076168031 hasRelatedWork W1989973775 @default.
• W2076168031 hasRelatedWork W2025722191 @default.
• W2076168031 hasRelatedWork W2080144430 @default.
• W2076168031 hasRelatedWork W2757504816 @default.
• W2076168031 hasRelatedWork W2759263422 @default.
• W2076168031 hasRelatedWork W2766605844 @default.
• W2076168031 hasRelatedWork W2896363115 @default.

• next