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- W2082792014 abstract "L’atteinte vasculaire de la sarcoïdose, très rare, est caractérisée, comme la maladie de Takayasu, par une localisation préférentielle aux vaisseaux de gros calibre. La discrimination entre les deux affections est de ce fait difficile. L’association de ces deux maladies rares ne peut être une simple coïncidence ; elle suggère l’existence d’un socle étiopathogénique commun et interroge la position nosographique de la maladie de Takayasu (maladie ou syndrome relevant d’étiologies variées ?). Nous rapportons le cas d’un patient atteint d’une sarcoïdose cutanéopulmonaire compliquée après plusieurs années par des signes d’ischémie aiguë du membre supérieur droit dans un tableau évocateur de maladie de Takayasu. Une réponse clinique favorable était observée sous l’association corticothérapie générale et méthotrexate. Cette observation permet de discuter les rapports entre la maladie de Takayasu et la sarcoïdose et d’alerter le clinicien sur la survenue possible d’une artérite granulomateuse au cours de la sarcoïdose, réclamant une prise en charge spécifique. Vascular involvement in sarcoidosis is very rare and is characterized by preferential involvement of large vessels similar to that observed in Takayasu's disease. Distinguishing between these two diseases is often difficult and constitutes a diagnostic pitfall. The association between sarcoidosis and Takayasu's arteritis is not coincidental and a common physiopathological factor may exist; it suggests a possible aetiopathogenetic relationship between sarcoidosis and Takayasu's arteritis and casts doubt on whether this form of vasculitis is a disease in its own right or simply a syndrome caused by other diseases. We report the case of a man with a 10-year history of cutaneous and pulmonary sarcoidosis who developed ischaemia of the right upper limb evocative of Takayasu's arteritis. The patient was successfully treated with oral steroids and methotrexate. This case prompts discussion about the relationship between Takayasu's disease and sarcoidosis. Physicians should be aware of the possible occurrence of granulomatous arteritis during the course of sarcoidosis which requires a special work-up." @default.
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- W2082792014 date "2009-12-01" @default.
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- W2082792014 title "Angéite granulomateuse au cours d’une sarcoïdose : maladie de Takayasu ?" @default.
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- W2082792014 doi "https://doi.org/10.1016/j.annder.2009.03.021" @default.
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