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- W2090000915 abstract "Kawasaki disease (KD) is a clinical pathological entity of unknown cause. Many investigators have proposed an infectious etiology. The pathological findings in KD and Pseudomonas septicemia have remarkable similarities. In both diseases a diffuse vascular involvement with little acute inflammatory reaction occurs, with necrosis and fibrin exudation in and around vessel walls. We suggested that Pseudomonas sepsis might play a role in the pathogenesis of KD. We embarked on a series of experimental investigations aiming at the production of a disease process similar to KD by infecting animals with Pseudomonas bacilli (mucoid and non-mucoid strains). Treatment of mice and guinea-pigs previously infected with 108 organisms intra-peritoneally with either nitrogen-mustard or cyclophosphamide produced a slow disease. At the end of the second week, these animals exhibited severe vasculitis with little inflammatory reaction. Dilatation of blood vessels and formation of coronary aneurysms were obtained similar to the histological findings in patients with KD. It is proposed that Pseudomonas aeruginosa infection in immunologically deficient animals, can mimic KD and a similar mechanism might be effective in the naturally occurring disease." @default.
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- W2090000915 date "1984-04-01" @default.
- W2090000915 modified "2023-09-26" @default.
- W2090000915 title "AN ANIMAL MODEL OF KAWASAKI DISEASE" @default.
- W2090000915 doi "https://doi.org/10.1203/00006450-198404001-01172" @default.
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