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- W2091034992 abstract "La alcaptonuria es una enfermedad metabólica hereditaria caracterizada por la tríada: orina oscura, pigmentación del tejido conectivo (ocronosis) y artritis degenerativa de las articulaciones de carga. Presentamos dos casos de artropatía ocronótica tratados mediante artroplastia. Dado que en la actualidad no existe ningún tratamiento médico que pueda frenar o revertir este proceso metabólico, las artroplastias son hasta el momento una buena opción terapéutica en casos evolucionados de afectación articular. Alkaptonuria is a hereditary metabolic disease, characterised by the triad: dark urine, connective tissue pigmentation (ochronosis) and degenerative arthritis of the weight-bearing joints. We present two cases of ochronotic arthropathy treated by arthroplasty. Given that there is currently no medical treatment that can halt or reverse this metabolic process, arthroplasties, are, at present, a good therapeutic option in cases that have progressed to joint involvement." @default.
- W2091034992 created "2016-06-24" @default.
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- W2091034992 date "2010-11-01" @default.
- W2091034992 modified "2023-09-26" @default.
- W2091034992 title "Artropatía ocronótica: a propósito de 2 casos" @default.
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- W2091034992 doi "https://doi.org/10.1016/j.recot.2010.08.004" @default.
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