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- W2092086199 abstract "La aplasia cutis congénita es una alteración presente al nacimiento, caracterizada por un defecto focal de piel y en ocasiones de estructuras subyacentes, de localización variable pero más frecuente en el cuero cabelludo. La etiología es desconocida y presenta cierto predominio por el sexo femenino. Se presenta como un defecto único o múltiple, de forma aislada o formando parte de síndromes más complejos de carácter familiar y, en menor medida, de carácter espontáneo. El pronóstico y el tratamiento dependen de la extensión y profundidad de las lesiones. Aplasia cutis congenita (ACC) is a skin defect present at birth affecting a focal area and sometimes underlying structures. Localization varies but the most frequently affected area is the scalp. The etiology is unknown and females are more commonly affected than males. This entity can manifest as a solitary defect or as multiple lesions. ACC can occur as an isolated defect, but can also be associated with other, more complex familial syndromes; sporadic cases are less frequent. Prognosis and treatment depend on the size and depth of the lesions." @default.
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- W2092086199 date "2008-07-01" @default.
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- W2092086199 title "Aplasia cutis congénita de calota" @default.
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- W2092086199 doi "https://doi.org/10.1016/s0304-5013(08)71110-5" @default.
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