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- W2092612142 endingPage "141" @default.
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- W2092612142 abstract "The discovery of dystrophin and its definition as the causative molecule in Duchenne Muscular Dystrophy has led to a renewed interest in the molecular structure of the muscle fiber plasma membrane and its association with the extracellular basal lamina. The original identification of dystrophin gave credence to the possibility that the plasma membrane of the muscle fiber may be highly organized and involved in maintaining appropriate homeostasis in this actively contracting cellular system. In this review, we examine the currently known members of the muscle fiber plasma membrane cytoskeleton and the interactions that occur between the different members of this complex using histological, electron microscopic, and confocal methods. From our studies and others cited in this review, it is clear that the dystrophin cytoskeletal complex is not completely understood and component molecules continue to be discovered. Perhaps equally importantly, currently defined molecules (such as alpha-actinin or neuronal nitric oxide synthase) are being recognized as being specifically associated with the complex. What is striking from all of the studies, to date, is that while we are able to identify members of the dystrophin cytoskeletal complex and while we are able to associate mutations of individual molecules with disease(s), we are still unable to truly define the roles of each of the molecules in maintaining the normal physiology of the muscle fiber." @default.
- W2092612142 created "2016-06-24" @default.
- W2092612142 creator A5020468998 @default.
- W2092612142 creator A5070266072 @default.
- W2092612142 creator A5086088688 @default.
- W2092612142 creator A5088924932 @default.
- W2092612142 date "2000-02-01" @default.
- W2092612142 modified "2023-09-23" @default.
- W2092612142 title "Plasma membrane cytoskeleton of muscle: a fine structural analysis" @default.
- W2092612142 cites W1504372166 @default.
- W2092612142 cites W1520280988 @default.
- W2092612142 cites W1525849227 @default.
- W2092612142 cites W1564301159 @default.
- W2092612142 cites W1575992755 @default.
- W2092612142 cites W1593294300 @default.
- W2092612142 cites W1600589392 @default.
- W2092612142 cites W1883425081 @default.
- W2092612142 cites W1890132633 @default.
- W2092612142 cites W1932376991 @default.
- W2092612142 cites W1966034267 @default.
- W2092612142 cites W1967261851 @default.
- W2092612142 cites W1968666078 @default.
- W2092612142 cites W1968957805 @default.
- W2092612142 cites W1972475548 @default.
- W2092612142 cites W1973552754 @default.
- W2092612142 cites W1973774525 @default.
- W2092612142 cites W1974473484 @default.
- W2092612142 cites W1974745886 @default.
- W2092612142 cites W1979901925 @default.
- W2092612142 cites W1981774688 @default.
- W2092612142 cites W1981850472 @default.
- W2092612142 cites W1984111138 @default.
- W2092612142 cites W1985292788 @default.
- W2092612142 cites W1985473631 @default.
- W2092612142 cites W1985549125 @default.
- W2092612142 cites W1985954761 @default.
- W2092612142 cites W1986168271 @default.
- W2092612142 cites W1987993105 @default.
- W2092612142 cites W1990585109 @default.
- W2092612142 cites W1994599070 @default.
- W2092612142 cites W1994805392 @default.
- W2092612142 cites W1997489050 @default.
- W2092612142 cites W2007755400 @default.
- W2092612142 cites W2008115339 @default.
- W2092612142 cites W2008741744 @default.
- W2092612142 cites W2008980136 @default.
- W2092612142 cites W2013960456 @default.
- W2092612142 cites W2014026136 @default.
- W2092612142 cites W2017854475 @default.
- W2092612142 cites W2018096072 @default.
- W2092612142 cites W2018248908 @default.
- W2092612142 cites W2020217527 @default.
- W2092612142 cites W2021202201 @default.
- W2092612142 cites W2024322464 @default.
- W2092612142 cites W2024364295 @default.
- W2092612142 cites W2026355265 @default.
- W2092612142 cites W2028134688 @default.
- W2092612142 cites W2031068195 @default.
- W2092612142 cites W2031263995 @default.
- W2092612142 cites W2031806916 @default.
- W2092612142 cites W2033491178 @default.
- W2092612142 cites W2034016438 @default.
- W2092612142 cites W2034619486 @default.
- W2092612142 cites W2036052070 @default.
- W2092612142 cites W2037023946 @default.
- W2092612142 cites W2038166560 @default.
- W2092612142 cites W2040418570 @default.
- W2092612142 cites W2041812736 @default.
- W2092612142 cites W2042054187 @default.
- W2092612142 cites W2042935017 @default.
- W2092612142 cites W2046905243 @default.
- W2092612142 cites W2047400703 @default.
- W2092612142 cites W2051292785 @default.
- W2092612142 cites W2056104802 @default.
- W2092612142 cites W2056376846 @default.
- W2092612142 cites W2059155059 @default.
- W2092612142 cites W2059255029 @default.
- W2092612142 cites W2059330693 @default.
- W2092612142 cites W2059837309 @default.
- W2092612142 cites W2062368768 @default.
- W2092612142 cites W2064385916 @default.
- W2092612142 cites W2065704959 @default.
- W2092612142 cites W2066180106 @default.
- W2092612142 cites W2067428261 @default.
- W2092612142 cites W2067592540 @default.
- W2092612142 cites W2070334431 @default.
- W2092612142 cites W2072491010 @default.
- W2092612142 cites W2073481346 @default.
- W2092612142 cites W2077687259 @default.
- W2092612142 cites W2078032311 @default.
- W2092612142 cites W2079543668 @default.
- W2092612142 cites W2081550861 @default.
- W2092612142 cites W2082798564 @default.
- W2092612142 cites W2089305683 @default.
- W2092612142 cites W2090537102 @default.
- W2092612142 cites W2090591739 @default.
- W2092612142 cites W2091233885 @default.
- W2092612142 cites W2091292897 @default.