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- W2092642018 abstract "Amyotrophic lateral sclerosis: update and new developments Ashley J Pratt1, Elizabeth D Getzoff1, J Jefferson P Perry1,21Department of Molecular Biology and The Skaggs Institute for Chemical Biology, The Scripps Research Institute, La Jolla, CA 92037, USA; 2The School of Biotechnology, Amrita University, Kollam, Kerala 690525, IndiaAbstract: Amyotrophic lateral sclerosis (ALS) is the most common form of motor neuron disease. It is typically characterized by adult-onset degeneration of the upper and lower motor neurons, and is usually fatal within a few years of onset. A subset of ALS patients has an inherited form of the disease, and a few of the known mutant genes identified in familial cases have also been found in sporadic forms of ALS. Precisely how the diverse ALS-linked gene products dictate the course of the disease, resulting in compromised voluntary muscular ability, is not entirely known. This review addresses the major advances that are being made in our understanding of the molecular mechanisms giving rise to the disease, which may eventually translate into new treatment options.Keywords: amyotrophic lateral sclerosis, neurodegeneration, motor neuron disease, genetics, aging" @default.
- W2092642018 created "2016-06-24" @default.
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- W2092642018 date "2012-02-01" @default.
- W2092642018 modified "2023-10-01" @default.
- W2092642018 title "Amyotrophic lateral sclerosis: update and new developments" @default.
- W2092642018 cites W1499705462 @default.
- W2092642018 cites W1504486296 @default.
- W2092642018 cites W1511318907 @default.
- W2092642018 cites W1523693806 @default.
- W2092642018 cites W1554056672 @default.
- W2092642018 cites W1558795029 @default.
- W2092642018 cites W1570509125 @default.
- W2092642018 cites W1576866620 @default.
- W2092642018 cites W1593896989 @default.
- W2092642018 cites W1619082318 @default.
- W2092642018 cites W1853392031 @default.
- W2092642018 cites W1940436875 @default.
- W2092642018 cites W1963544390 @default.
- W2092642018 cites W1965237975 @default.
- W2092642018 cites W1965302033 @default.
- W2092642018 cites W1968683040 @default.
- W2092642018 cites W1968735793 @default.
- W2092642018 cites W1973456315 @default.
- W2092642018 cites W1974181990 @default.
- W2092642018 cites W1974809155 @default.
- W2092642018 cites W1975549226 @default.
- W2092642018 cites W1975695493 @default.
- W2092642018 cites W1976765363 @default.
- W2092642018 cites W197705081 @default.
- W2092642018 cites W1978849123 @default.
- W2092642018 cites W1979179514 @default.
- W2092642018 cites W1979342442 @default.
- W2092642018 cites W1979530693 @default.
- W2092642018 cites W1979744772 @default.
- W2092642018 cites W1979837223 @default.
- W2092642018 cites W1983386027 @default.
- W2092642018 cites W1983541649 @default.
- W2092642018 cites W1983560493 @default.
- W2092642018 cites W1985279637 @default.
- W2092642018 cites W1990470345 @default.
- W2092642018 cites W1991208268 @default.
- W2092642018 cites W1992827214 @default.
- W2092642018 cites W1995163274 @default.
- W2092642018 cites W1996703483 @default.
- W2092642018 cites W1996904797 @default.
- W2092642018 cites W2002502450 @default.
- W2092642018 cites W2002903119 @default.
- W2092642018 cites W2003618511 @default.
- W2092642018 cites W2006127490 @default.
- W2092642018 cites W2007336957 @default.
- W2092642018 cites W2009030515 @default.
- W2092642018 cites W2009225398 @default.
- W2092642018 cites W2011184139 @default.
- W2092642018 cites W2012851706 @default.
- W2092642018 cites W2013154697 @default.
- W2092642018 cites W2013357523 @default.
- W2092642018 cites W2015037203 @default.
- W2092642018 cites W2016123870 @default.
- W2092642018 cites W2017111955 @default.
- W2092642018 cites W2019031549 @default.
- W2092642018 cites W2020776414 @default.
- W2092642018 cites W2021988387 @default.
- W2092642018 cites W2022853768 @default.
- W2092642018 cites W2023556666 @default.
- W2092642018 cites W2026667906 @default.
- W2092642018 cites W2027742580 @default.
- W2092642018 cites W2027925622 @default.
- W2092642018 cites W2029303246 @default.
- W2092642018 cites W2031964319 @default.
- W2092642018 cites W2032321301 @default.
- W2092642018 cites W2034651824 @default.
- W2092642018 cites W2040239669 @default.
- W2092642018 cites W2040592121 @default.
- W2092642018 cites W2040621074 @default.
- W2092642018 cites W2041185112 @default.
- W2092642018 cites W2043517717 @default.
- W2092642018 cites W2044638164 @default.
- W2092642018 cites W2047139561 @default.
- W2092642018 cites W2048813950 @default.
- W2092642018 cites W2049342904 @default.
- W2092642018 cites W2049928253 @default.
- W2092642018 cites W2049958331 @default.
- W2092642018 cites W2050783261 @default.
- W2092642018 cites W2051401615 @default.
- W2092642018 cites W2052888134 @default.
- W2092642018 cites W2053362200 @default.
- W2092642018 cites W2055456084 @default.
- W2092642018 cites W2056937466 @default.
- W2092642018 cites W2057139034 @default.
- W2092642018 cites W2059355164 @default.
- W2092642018 cites W2060537202 @default.
- W2092642018 cites W2061044120 @default.
- W2092642018 cites W2061420456 @default.
- W2092642018 cites W2063067835 @default.
- W2092642018 cites W2063183749 @default.