Matches in SemOpenAlex for { <https://semopenalex.org/work/W2096702246> ?p ?o ?g. }
Showing items 1 to 74 of
74
with 100 items per page.
- W2096702246 endingPage "66" @default.
- W2096702246 startingPage "61" @default.
- W2096702246 abstract "Glycosaminoglycan isolated from urine of a patient with the Hurler-Scheie compound syndrome consisted of dermatan sulfate (60%), heparan sulfate (34%) and chondroitin sulfate (6%). About 60% of both dermatan and chondroitin sulfates had molecular weight 8,000-10,000, while 95% of the heparan sulfate had molecular weight less than 6,000. The total sulfate content of the glycosaminoglycans increased with decrease in molecular weight. N-sulfate content in the heparan sulfate, however, had no relation to molecular weight, and was 0.33 mole per mole of glucosamine on the average. About 70% of the heparan sulfate with the lowest molecular weight (1,500) were composed of three repeating disaccharide units of heparan sulfate and two acetyl, one N-sulfate and three O-sulfate groups linked to the units. The dermatan sulfate contained 1.0-1.2 moles of sulfate per mole of galactosamine. Of the excess sulfate 45-65% were bound to iduronate residues and the rest to C-6 of N-acetylgalactosamine 4-sulfate residues. Most of the dermatan sulfate (83.2-100%) had nonsulfated iduronic acid at the non-reducing end. This finding is consistent with the defect of iduronidase in this disease." @default.
- W2096702246 created "2016-06-24" @default.
- W2096702246 creator A5050812124 @default.
- W2096702246 creator A5070829886 @default.
- W2096702246 creator A5072774983 @default.
- W2096702246 creator A5088847505 @default.
- W2096702246 date "1982-01-01" @default.
- W2096702246 modified "2023-09-27" @default.
- W2096702246 title "Characteristics of urinay glycosaminoglycans excreted by a patient with the Hurler-Scheie compound syndrome." @default.
- W2096702246 cites W1976144161 @default.
- W2096702246 cites W1979279528 @default.
- W2096702246 cites W1982205258 @default.
- W2096702246 cites W1990534656 @default.
- W2096702246 doi "https://doi.org/10.1620/tjem.136.61" @default.
- W2096702246 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/6803394" @default.
- W2096702246 hasPublicationYear "1982" @default.
- W2096702246 type Work @default.
- W2096702246 sameAs 2096702246 @default.
- W2096702246 citedByCount "2" @default.
- W2096702246 countsByYear W20967022462012 @default.
- W2096702246 crossrefType "journal-article" @default.
- W2096702246 hasAuthorship W2096702246A5050812124 @default.
- W2096702246 hasAuthorship W2096702246A5070829886 @default.
- W2096702246 hasAuthorship W2096702246A5072774983 @default.
- W2096702246 hasAuthorship W2096702246A5088847505 @default.
- W2096702246 hasBestOaLocation W20967022461 @default.
- W2096702246 hasConcept C100817775 @default.
- W2096702246 hasConcept C153074725 @default.
- W2096702246 hasConcept C178790620 @default.
- W2096702246 hasConcept C185592680 @default.
- W2096702246 hasConcept C2776648616 @default.
- W2096702246 hasConcept C2777346074 @default.
- W2096702246 hasConcept C2778041096 @default.
- W2096702246 hasConcept C2778066728 @default.
- W2096702246 hasConcept C2778125326 @default.
- W2096702246 hasConcept C2778343803 @default.
- W2096702246 hasConcept C2779553658 @default.
- W2096702246 hasConcept C2779650520 @default.
- W2096702246 hasConcept C55493867 @default.
- W2096702246 hasConceptScore W2096702246C100817775 @default.
- W2096702246 hasConceptScore W2096702246C153074725 @default.
- W2096702246 hasConceptScore W2096702246C178790620 @default.
- W2096702246 hasConceptScore W2096702246C185592680 @default.
- W2096702246 hasConceptScore W2096702246C2776648616 @default.
- W2096702246 hasConceptScore W2096702246C2777346074 @default.
- W2096702246 hasConceptScore W2096702246C2778041096 @default.
- W2096702246 hasConceptScore W2096702246C2778066728 @default.
- W2096702246 hasConceptScore W2096702246C2778125326 @default.
- W2096702246 hasConceptScore W2096702246C2778343803 @default.
- W2096702246 hasConceptScore W2096702246C2779553658 @default.
- W2096702246 hasConceptScore W2096702246C2779650520 @default.
- W2096702246 hasConceptScore W2096702246C55493867 @default.
- W2096702246 hasIssue "1" @default.
- W2096702246 hasLocation W20967022461 @default.
- W2096702246 hasLocation W20967022462 @default.
- W2096702246 hasOpenAccess W2096702246 @default.
- W2096702246 hasPrimaryLocation W20967022461 @default.
- W2096702246 hasRelatedWork W2058596779 @default.
- W2096702246 hasRelatedWork W2096702246 @default.
- W2096702246 hasRelatedWork W2121271975 @default.
- W2096702246 hasRelatedWork W2150247380 @default.
- W2096702246 hasRelatedWork W2278859991 @default.
- W2096702246 hasRelatedWork W2463006850 @default.
- W2096702246 hasRelatedWork W2489519486 @default.
- W2096702246 hasRelatedWork W2526931775 @default.
- W2096702246 hasRelatedWork W52252934 @default.
- W2096702246 hasRelatedWork W55321852 @default.
- W2096702246 hasVolume "136" @default.
- W2096702246 isParatext "false" @default.
- W2096702246 isRetracted "false" @default.
- W2096702246 magId "2096702246" @default.
- W2096702246 workType "article" @default.