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- W2105082539 abstract "The macrophage activation syndrome is a rare but potentially fatal complication of patients with autoimmune rheumatic diseases. This is a clinicopathological entity characterized by activation of histiocytes with prominent hemophagocytosis in the bone marrow and other reticuloendothelial systems. In patients with lupus it may mimic an exacerbation of the disease or infection. We report the case of a 7-year-old girl in whom the diagnosis of lupus erythematosus and macrophage activation syndrome was simultaneously made with response to the use of cyclophosphamide." @default.
- W2105082539 created "2016-06-24" @default.
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- W2105082539 date "2014-09-01" @default.
- W2105082539 modified "2023-10-18" @default.
- W2105082539 title "Macrophage Activation Syndrome as the Initial Manifestation of Severe Juvenile Onset Systemic Lupus Erythematosus. Favorable Response to Cyclophosphamide" @default.
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- W2105082539 doi "https://doi.org/10.1016/j.reumae.2013.12.009" @default.
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