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- W2110308047 abstract "Pulmonary veno-occlusive disease (PVOD) is a rare form of pulmonary hypertension that may develop in patients with connective tissue diseases (CTD). Most cases have been reported in patients with systemic sclerosis, though associations with systemic lupus erythematosis and mixed connective tissue disease have also been described. PVOD is characterised by progressive obstruction of small pulmonary veins and venules that leads to increased pulmonary vascular resistance, right heart failure and premature death. Distinguishing PVOD from pulmonary arterial hypertension (PAH) is often difficult, though use of a diagnostic algorithm may improve diagnostic accuracy and preclude recourse to lung biopsy. The finding of normal left-heart filling pressures in the context of radiological studies suggestive of pulmonary oedema is an important diagnostic clue, particularly if this clinical scenario coincides with the introduction of vasodilator therapy. There are no approved treatments for the disorder, though cautious use of PAH specific therapy may improve short-term outcomes in selected idiopathic PVOD cases. This review summarises the epidemiologic, clinico-pathologic and imaging characteristics of PVOD in the setting of CTD and discusses potential management approaches." @default.
- W2110308047 created "2016-06-24" @default.
- W2110308047 creator A5007247451 @default.
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- W2110308047 date "2011-01-01" @default.
- W2110308047 modified "2023-10-01" @default.
- W2110308047 title "Pulmonary veno-occlusive disease: The bête noire of pulmonary hypertension in connective tissue diseases?" @default.
- W2110308047 cites W1497601632 @default.
- W2110308047 cites W1553685319 @default.
- W2110308047 cites W1556252963 @default.
- W2110308047 cites W1964639503 @default.
- W2110308047 cites W1978752282 @default.
- W2110308047 cites W1983598259 @default.
- W2110308047 cites W1988702633 @default.
- W2110308047 cites W1989333364 @default.
- W2110308047 cites W1991534547 @default.
- W2110308047 cites W1991971500 @default.
- W2110308047 cites W1992166749 @default.
- W2110308047 cites W1992320083 @default.
- W2110308047 cites W1997510827 @default.
- W2110308047 cites W1998123371 @default.
- W2110308047 cites W1999737200 @default.
- W2110308047 cites W2000394214 @default.
- W2110308047 cites W2001776029 @default.
- W2110308047 cites W2002982360 @default.
- W2110308047 cites W2003018235 @default.
- W2110308047 cites W2003963025 @default.
- W2110308047 cites W2005131496 @default.
- W2110308047 cites W2007927680 @default.
- W2110308047 cites W2009749954 @default.
- W2110308047 cites W2010028334 @default.
- W2110308047 cites W2016925103 @default.
- W2110308047 cites W2018605757 @default.
- W2110308047 cites W2018759973 @default.
- W2110308047 cites W2020700433 @default.
- W2110308047 cites W2023935277 @default.
- W2110308047 cites W2024972836 @default.
- W2110308047 cites W2029788843 @default.
- W2110308047 cites W2033069964 @default.
- W2110308047 cites W2037507514 @default.
- W2110308047 cites W2038485127 @default.
- W2110308047 cites W2041315674 @default.
- W2110308047 cites W2045573491 @default.
- W2110308047 cites W2045649696 @default.
- W2110308047 cites W2051302134 @default.
- W2110308047 cites W2052522225 @default.
- W2110308047 cites W2053553238 @default.
- W2110308047 cites W2055147321 @default.
- W2110308047 cites W2056861453 @default.
- W2110308047 cites W2060969781 @default.
- W2110308047 cites W2062002285 @default.
- W2110308047 cites W2063332721 @default.
- W2110308047 cites W2067182224 @default.
- W2110308047 cites W2069038734 @default.
- W2110308047 cites W2077138985 @default.
- W2110308047 cites W2083401634 @default.
- W2110308047 cites W2084749196 @default.
- W2110308047 cites W2088682646 @default.
- W2110308047 cites W2090526551 @default.
- W2110308047 cites W2096751910 @default.
- W2110308047 cites W2097973238 @default.
- W2110308047 cites W2104612376 @default.
- W2110308047 cites W2106720570 @default.
- W2110308047 cites W2106805951 @default.
- W2110308047 cites W2110112636 @default.
- W2110308047 cites W2113479198 @default.
- W2110308047 cites W2121599003 @default.
- W2110308047 cites W2124715046 @default.
- W2110308047 cites W2125833821 @default.
- W2110308047 cites W2127994875 @default.
- W2110308047 cites W2128547912 @default.
- W2110308047 cites W2129392822 @default.
- W2110308047 cites W2129894155 @default.
- W2110308047 cites W2135153573 @default.
- W2110308047 cites W2135510321 @default.
- W2110308047 cites W2141262339 @default.
- W2110308047 cites W2142622392 @default.
- W2110308047 cites W2144429046 @default.
- W2110308047 cites W2145247983 @default.
- W2110308047 cites W2146707899 @default.
- W2110308047 cites W2149839143 @default.
- W2110308047 cites W2150226364 @default.
- W2110308047 cites W2150891082 @default.
- W2110308047 cites W2154361445 @default.
- W2110308047 cites W2157488331 @default.
- W2110308047 cites W2158518028 @default.
- W2110308047 cites W2159677723 @default.
- W2110308047 cites W2170072326 @default.
- W2110308047 cites W2170533606 @default.
- W2110308047 cites W2321522617 @default.
- W2110308047 cites W2418706503 @default.
- W2110308047 cites W2486869454 @default.