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- W2118775107 abstract "Multiple system atrophy (MSA) is a sporadic, adult-onset neurodegenerative disease, which is characterized by striatonigral degeneration, olivopontocerebellar atrophy, and preganglionic autonomic lesions in any combination. The histological hallmark is the presence of argyrophilic fibrillary inclusions in the oligodendrocytes, referred to as glial cytoplasmic inclusions (GCIs). Fibrillary inclusions are also found in the neuronal somata, axons, and nucleus. Neuronal cytoplasmic inclusions are frequently found in the pontine and inferior olivary nuclei. Since the discovery of alpha-synuclein as a major component of glial and neuronal inclusions in MSA, two neurodegenerative processes have been considered in this disease: one is due to the widespread occurrence of GCIs associated with oligodendroglia-myelin degeneration (oligodendrogliopathy) in the central nervous system, and the other is due to the filamentous aggregation of alpha-synuclein in the neurons in several brain regions. These two degenerative processes might synergistically cause neuronal depletion in MSA." @default.
- W2118775107 created "2016-06-24" @default.
- W2118775107 creator A5000409879 @default.
- W2118775107 creator A5067901270 @default.
- W2118775107 date "2006-08-01" @default.
- W2118775107 modified "2023-09-24" @default.
- W2118775107 title "Cellular pathology in multiple system atrophy" @default.
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- W2118775107 doi "https://doi.org/10.1111/j.1440-1789.2006.00713.x" @default.
- W2118775107 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/16961071" @default.
- W2118775107 hasPublicationYear "2006" @default.
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