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- W2124803404 endingPage "544" @default.
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- W2124803404 abstract "Increased serum eosinophil levels have been associated with multiple disorders of immune deficiency or immune dysregulation. Although primary immunodeficiency diseases are rare, it is important to consider these in the differential diagnosis of patients with eosinophilia. In this review, the clinical features, laboratory findings, diagnosis, and genetic basis of disease of several disorders of immune deficiency or dysregulation are discussed. The article includes autosomal dominant hyper IgE syndrome, DOCK8 deficiency, phosphoglucomutase 3 deficiency, ADA-SCID, Omenn syndrome, Wiskott-Aldrich syndrome, Loeys-Dietz syndrome, autoimmune lymphoproliferative syndrome, immunodysregulation, polyendocrinopathy, enteropathy, X-linked syndrome, Comel-Netherton syndrome, and severe dermatitis, multiple allergies, and metabolic wasting syndrome." @default.
- W2124803404 created "2016-06-24" @default.
- W2124803404 creator A5002507553 @default.
- W2124803404 creator A5054348599 @default.
- W2124803404 creator A5063867007 @default.
- W2124803404 date "2015-08-01" @default.
- W2124803404 modified "2023-10-18" @default.
- W2124803404 title "Eosinophilia Associated with Disorders of Immune Deficiency or Immune Dysregulation" @default.
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