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- W2134879438 endingPage "472" @default.
- W2134879438 startingPage "455" @default.
- W2134879438 abstract "Inherited platelet disorders encompass a heterogeneous group of bleeding disorders where a variety of molecular defects can affect platelet number, function or both. The defects involve deficiencies or dysfunction of platelet receptors, signaling pathways, cytoskeletal proteins, granule contents and abnormalities in procoagulant activity. These disorders can be difficult to distinguish clinically as they present with the common symptom of mucocutaneous bleeding. Inherited thrombocytopenia needs to be considered in all patients suspected of having primary immune thrombocytopenia, where platelets may also have functional defects. After a careful history and physical examination, initial investigations include a complete blood count with a peripheral smear, followed by appropriate specific investigations that often require specialized referral centers. This article is a summary of the current data on clinical presentation, pathogenesis, diagnosis and management of inherited platelet disorders." @default.
- W2134879438 created "2016-06-24" @default.
- W2134879438 creator A5004205333 @default.
- W2134879438 creator A5007924387 @default.
- W2134879438 creator A5088699247 @default.
- W2134879438 date "2011-08-01" @default.
- W2134879438 modified "2023-10-13" @default.
- W2134879438 title "Inherited platelet disorders: a clinical approach to diagnosis and management" @default.
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