Matches in SemOpenAlex for { <https://semopenalex.org/work/W2136816237> ?p ?o ?g. }
- W2136816237 abstract "In children the rare autoimmune skin diseases pemphigus, pemphigoid and epidermolysis bullosa acquisita and their variants may occur. Unfortunately, delay in diagnosis occurs frequently. In these dermatoses, antibodies are formed against one of the antigens involved in cell adhesion within either intercellular epidermal cells or the epidermal basement membrane zone. This antibody formation eventually leads to blistering of the skin and/or the stratified epithelium of mucous membranes. In children with these diseases, systemic treatment with prednisone is often necessary to induce remission of the disease; in serious cases, the addition of azathioprine, cyclophosphamide, intravenous immunoglobulines or rituximab may be needed. In some cases, topical corticosteroids or oral dapsone suffice. In most cases the prognosis quoad vitam is good, but the general prognosis is variable and sometimes lifelong treatment may be necessary." @default.
- W2136816237 created "2016-06-24" @default.
- W2136816237 creator A5083484570 @default.
- W2136816237 creator A5086077564 @default.
- W2136816237 date "2011-05-24" @default.
- W2136816237 modified "2023-09-26" @default.
- W2136816237 title "Pemphigus, Pemphigoid and Epidermolysis Bullosa Acquisita" @default.
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