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- W2144855464 endingPage "1128" @default.
- W2144855464 startingPage "1122" @default.
- W2144855464 abstract "Abstract Organisms living under aerobic conditions need oxygen for the metabolic conversion of nutrition into energy. With the appearance of increasingly complex animals, a specialized transport system (erythrocytes) arose during evolution to provide oxygen to virtually every single cell in the body. Moreover, in case of low environmental partial pressure of oxygen, the number of erythrocytes automatically increases to preserve sustained oxygen delivery. This process relies predominantly on the cytokine erythropoietin (Epo) and its transcription factor hypoxia inducible factor (HIF), whereas the von Hippel-Lindau (VHL) ubiquitin ligase as well as the oxygen-sensitive prolyl hydroxylases (PHDs) represent essential regulators of this oxygen-sensing system. Deregulation of particular members of this pathway (eg, PHD2, HIF2α, VHL) lead to disorders in blood homeostasis as a result of insufficient (anemia) or excessive (erythrocytosis) red blood cell production." @default.
- W2144855464 created "2016-06-24" @default.
- W2144855464 creator A5004739251 @default.
- W2144855464 creator A5014391609 @default.
- W2144855464 creator A5019412191 @default.
- W2144855464 date "2013-08-15" @default.
- W2144855464 modified "2023-10-13" @default.
- W2144855464 title "Erythrocytosis: the HIF pathway in control" @default.
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