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- W2149295364 abstract "La deficiencia de piruvato cinasa es una causa rara de anemia hemolítica. Durante el embarazo, se ha tratado casos graves de esta deficiencia con transfusions profilácticas de concentrados de hematíes para mantener unos valores de hemoglobina entre 7 y 8 g/dl. Se descubrió un caso de anemia hemolítica secundaria a déficit de piruvato cinasa durante el primer embarazo de una mujer de 32 años. La anemia se trató con transfusiones de concentrados de hematíes, y en la segunda gestación fue necesario un mayor número de ellas para mantener los valores de hemoglobina por encima de 7 g/dl. En ambos casos, los recién nacidos tuvieron pesos en el percentil adecuado para su edad gestacional. Este tipo de anemia es raro, y en ocasiones se descubre en situaciones especiales, como embarazo, infección o estrés. Pyruvate kinase deficiency is a rare cause of hemolytic anemia. During pregnancy, severe cases have traditionally been treated with prophylactic blood transfusions to maintain the hemoglobin concentration above arbitrary thresholds of 7-8 g/dL. A case of hemolytic anemia due to pyruvate kinase deficiency was discovered during the first pregnancy of a 32-year-old woman. The anemia was treated with blood transfusions. In a second pregnancy, the patient required a greater number of transfusions to keep the hemoglobin concentration above 7 g/dL. Both newborns were healthy and had adequate birth weight for gestational age. This kind of anemia is rare and sometimes occurs in special situations such as pregnancy, infection, or stress." @default.
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- W2149295364 date "2006-06-01" @default.
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- W2149295364 title "Anemia secundaria a déficit de piruvato cinasa en sucesivas gestaciones" @default.
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- W2149295364 doi "https://doi.org/10.1016/s0210-573x(06)74097-7" @default.
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