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- W2149669580 endingPage "342" @default.
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- W2149669580 abstract "Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive, and usually fatal pulmonary disease for which there are no proven drug therapies. Anti-inflammatory and immunosuppressive agents have been largely ineffective. The precise relationship of IPF to other idiopathic interstitial pneumonias (IIPs) is not known, despite the observation that different histopathologic patterns of IIP may coexist in the same patient. We propose that these different histopathologic 'reaction' patterns may be determined by complex interactions between host and environmental factors that alter the local alveolar milieu. Recent paradigms in IPF pathogenesis have focused on dysregulated epithelial-mesenchymal interactions, an imbalance in T(H)1/T(H)2 cytokine profile and potential roles for aberrant angiogenesis. In this review, we discuss these evolving concepts in disease pathogenesis and emerging therapies designed to target pro-fibrogenic pathways in IPF." @default.
- W2149669580 created "2016-06-24" @default.
- W2149669580 creator A5022475245 @default.
- W2149669580 creator A5081550304 @default.
- W2149669580 date "2006-01-01" @default.
- W2149669580 modified "2023-10-14" @default.
- W2149669580 title "Idiopathic Pulmonary Fibrosis" @default.
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