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- W2151885904 endingPage "575" @default.
- W2151885904 startingPage "565" @default.
- W2151885904 abstract "The immunodeficiency in ataxia-telangiectasia (A-T) is highly variable. Laboratory abnormalities correlate poorly with susceptibility to infection and are almost exclusively restricted to patients with mutations resulting in no A-T mutated kinase activity. Opportunistic infections are unusual but sinopulmonary infections are common and can contribute to the development of pulmonary insufficiency. Preventing lung disease involves maximizing immunity, as well as measures to counteract the tendency to develop pulmonary aspiration, which increases with age. Immunizations should include pneumococcal conjugate, influenza and, in all but the most severely lymphopenic, measles, mumps, rubella, and varicella zoster vaccines. Prophylactic azithromycin is commonly used and believed to be useful, although a firm evidence base for its use in A-T is lacking. Approximately 12–15% of patients require regular immunoglobulin therapy. Further studies are required on potential disease-modulating therapies, such as antioxidants and corticosteroids. Strategies for the modulation of gene transcription remain at the preclinical laboratory stage." @default.
- W2151885904 created "2016-06-24" @default.
- W2151885904 creator A5041681218 @default.
- W2151885904 date "2009-09-01" @default.
- W2151885904 modified "2023-10-10" @default.
- W2151885904 title "Update on the management of the immunodeficiency in ataxia-telangiectasia" @default.
- W2151885904 cites W1487079135 @default.
- W2151885904 cites W1546331339 @default.
- W2151885904 cites W1555218304 @default.
- W2151885904 cites W1564315948 @default.
- W2151885904 cites W164752722 @default.
- W2151885904 cites W1654261328 @default.
- W2151885904 cites W1963673805 @default.
- W2151885904 cites W1965360670 @default.
- W2151885904 cites W1965782347 @default.
- W2151885904 cites W1967630574 @default.
- W2151885904 cites W1973086487 @default.
- W2151885904 cites W1976231348 @default.
- W2151885904 cites W1977923363 @default.
- W2151885904 cites W1978177909 @default.
- W2151885904 cites W1982570529 @default.
- W2151885904 cites W1984971166 @default.
- W2151885904 cites W1989768794 @default.
- W2151885904 cites W1990197342 @default.
- W2151885904 cites W1991221096 @default.
- W2151885904 cites W1992078876 @default.
- W2151885904 cites W1994873026 @default.
- W2151885904 cites W1995100225 @default.
- W2151885904 cites W1996461975 @default.
- W2151885904 cites W1997660879 @default.
- W2151885904 cites W1999286267 @default.
- W2151885904 cites W2000058086 @default.
- W2151885904 cites W2005015229 @default.
- W2151885904 cites W2006986940 @default.
- W2151885904 cites W2013473088 @default.
- W2151885904 cites W2017908487 @default.
- W2151885904 cites W2020058074 @default.
- W2151885904 cites W2020391807 @default.
- W2151885904 cites W2023148106 @default.
- W2151885904 cites W2025222765 @default.
- W2151885904 cites W2028292318 @default.
- W2151885904 cites W2028768933 @default.
- W2151885904 cites W2029807929 @default.
- W2151885904 cites W2032356166 @default.
- W2151885904 cites W2033011952 @default.
- W2151885904 cites W2033369951 @default.
- W2151885904 cites W2036339686 @default.
- W2151885904 cites W2037824526 @default.
- W2151885904 cites W2042357523 @default.
- W2151885904 cites W2042524696 @default.
- W2151885904 cites W2047624229 @default.
- W2151885904 cites W2049838261 @default.
- W2151885904 cites W2050435294 @default.
- W2151885904 cites W2052898620 @default.
- W2151885904 cites W2065592145 @default.
- W2151885904 cites W2066062775 @default.
- W2151885904 cites W2074204311 @default.
- W2151885904 cites W2079052854 @default.
- W2151885904 cites W2081719410 @default.
- W2151885904 cites W2082444880 @default.
- W2151885904 cites W2082604172 @default.
- W2151885904 cites W2090648579 @default.
- W2151885904 cites W2095202234 @default.
- W2151885904 cites W2105637045 @default.
- W2151885904 cites W2108631046 @default.
- W2151885904 cites W2109736767 @default.
- W2151885904 cites W2110817748 @default.
- W2151885904 cites W2116813766 @default.
- W2151885904 cites W2120134270 @default.
- W2151885904 cites W2122405873 @default.
- W2151885904 cites W2123356698 @default.
- W2151885904 cites W2126664265 @default.
- W2151885904 cites W2127604039 @default.
- W2151885904 cites W2127888537 @default.
- W2151885904 cites W2129297300 @default.
- W2151885904 cites W2131065276 @default.
- W2151885904 cites W2134925546 @default.
- W2151885904 cites W2136883575 @default.
- W2151885904 cites W2139099050 @default.
- W2151885904 cites W2139777089 @default.
- W2151885904 cites W2143570924 @default.
- W2151885904 cites W2144626514 @default.
- W2151885904 cites W2159168998 @default.
- W2151885904 cites W2164250623 @default.
- W2151885904 cites W2166852863 @default.
- W2151885904 cites W2168353929 @default.
- W2151885904 cites W2170052969 @default.
- W2151885904 cites W2170601039 @default.
- W2151885904 cites W2171476916 @default.
- W2151885904 cites W2313025745 @default.
- W2151885904 cites W2317029780 @default.
- W2151885904 cites W2410250208 @default.
- W2151885904 cites W2423679212 @default.
- W2151885904 cites W2623542670 @default.
- W2151885904 cites W265320334 @default.
- W2151885904 cites W4246776065 @default.
- W2151885904 cites W4250113329 @default.
- W2151885904 doi "https://doi.org/10.1586/eci.09.35" @default.