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- W2153287706 endingPage "328" @default.
- W2153287706 startingPage "319" @default.
- W2153287706 abstract "Transition metals are frequently used as cofactors for enzymes and oxygen-carrying proteins that take advantage of their propensity to gain and lose single electrons. Metals are particularly important in mitochondria, where they play essential roles in the production of ATP and detoxification of reactive oxygen species. At the same time, transition metals (particularly Fe and Cu) can promote the formation of harmful radicals, necessitating meticulous control of metal concentration and subcellular compartmentalization. We summarize our current understanding of Fe and Cu in mammalian mitochondrial biology and discuss human diseases associated with aberrations in mitochondrial metal homeostasis." @default.
- W2153287706 created "2016-06-24" @default.
- W2153287706 creator A5047497330 @default.
- W2153287706 creator A5067860430 @default.
- W2153287706 creator A5084835430 @default.
- W2153287706 date "2013-03-01" @default.
- W2153287706 modified "2023-10-14" @default.
- W2153287706 title "Iron and Copper in Mitochondrial Diseases" @default.
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