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- W2154256357 abstract "A wide variety of tumors can arise in the retina, having their origin either in retinal cells (retinocytes and glial cells), the retinal vasculature (vascular endothelium) or the retinal pigment epithelium. This article summarizes the clinical features of the retinal tumors that are encountered primarily in adults. With the advent of molecular genetic testing, the majority of these tumors can be associated with a genetic disorder, which further helps the early detection of associated pathologies in other organs. The best-known example is probably the von Hippel–Lindau syndrome, which is caused by a mutation of the VHL gene. The ophthalmologist is often the first physician to recognize and establish the diagnosis, since retinal capillary hemangioblastomas are commonly the first sign of this syndrome. Retinal astrocytomas are often associated with the tuberous sclerosis complex, combined hamartomas can be associated with neurofibromatosis type 1 or 2 and retinal pigment epithelium hamartomas can be associated with familial adenomatous polyposis coli, which is a condition known to predispose colon cancer; hence, the ophthalmologist can play a pivotal role in the early detection and treatment of a life-threatening disorder." @default.
- W2154256357 created "2016-06-24" @default.
- W2154256357 creator A5044742885 @default.
- W2154256357 creator A5076786068 @default.
- W2154256357 date "2011-06-01" @default.
- W2154256357 modified "2023-09-23" @default.
- W2154256357 title "Retinal tumors in adults: diagnosis and management" @default.
- W2154256357 cites W1549434051 @default.
- W2154256357 cites W1550566912 @default.
- W2154256357 cites W1574181941 @default.
- W2154256357 cites W1587986911 @default.
- W2154256357 cites W1599022175 @default.
- W2154256357 cites W1601063926 @default.
- W2154256357 cites W1693193785 @default.
- W2154256357 cites W1906591060 @default.
- W2154256357 cites W1936705254 @default.
- W2154256357 cites W1963981451 @default.
- W2154256357 cites W1964332087 @default.
- W2154256357 cites W1968957273 @default.
- W2154256357 cites W1969095582 @default.
- W2154256357 cites W1970561886 @default.
- W2154256357 cites W1970658259 @default.
- W2154256357 cites W1971387986 @default.
- W2154256357 cites W1975181125 @default.
- W2154256357 cites W1975480771 @default.
- W2154256357 cites W1982729641 @default.
- W2154256357 cites W1982977010 @default.
- W2154256357 cites W1983781484 @default.
- W2154256357 cites W1983792009 @default.
- W2154256357 cites W1985426105 @default.
- W2154256357 cites W1985557878 @default.
- W2154256357 cites W1986266940 @default.
- W2154256357 cites W1989040551 @default.
- W2154256357 cites W1989879796 @default.
- W2154256357 cites W1992047314 @default.
- W2154256357 cites W1992697111 @default.
- W2154256357 cites W1992954334 @default.
- W2154256357 cites W1995263811 @default.
- W2154256357 cites W1997923052 @default.
- W2154256357 cites W2001170648 @default.
- W2154256357 cites W2002675129 @default.
- W2154256357 cites W2004190746 @default.
- W2154256357 cites W2004517193 @default.
- W2154256357 cites W2006622472 @default.
- W2154256357 cites W2006901833 @default.
- W2154256357 cites W2007302794 @default.
- W2154256357 cites W2008337554 @default.
- W2154256357 cites W2008410368 @default.
- W2154256357 cites W2013519265 @default.
- W2154256357 cites W2016272598 @default.
- W2154256357 cites W2016822362 @default.
- W2154256357 cites W2018138697 @default.
- W2154256357 cites W2019472430 @default.
- W2154256357 cites W2021956975 @default.
- W2154256357 cites W2022846449 @default.
- W2154256357 cites W2023191770 @default.
- W2154256357 cites W2024307723 @default.
- W2154256357 cites W2024828959 @default.
- W2154256357 cites W2027800775 @default.
- W2154256357 cites W2028165861 @default.
- W2154256357 cites W2029355345 @default.
- W2154256357 cites W2031013001 @default.
- W2154256357 cites W2031126063 @default.
- W2154256357 cites W2033845419 @default.
- W2154256357 cites W2034194451 @default.
- W2154256357 cites W2037307704 @default.
- W2154256357 cites W2037895319 @default.
- W2154256357 cites W2038416809 @default.
- W2154256357 cites W2039075776 @default.
- W2154256357 cites W2039143533 @default.
- W2154256357 cites W2040092396 @default.
- W2154256357 cites W2043312477 @default.
- W2154256357 cites W2049105411 @default.
- W2154256357 cites W2051698483 @default.
- W2154256357 cites W2051997018 @default.
- W2154256357 cites W2054684186 @default.
- W2154256357 cites W2055106956 @default.
- W2154256357 cites W2055546200 @default.
- W2154256357 cites W2057771750 @default.
- W2154256357 cites W2060198816 @default.
- W2154256357 cites W2060648460 @default.
- W2154256357 cites W2062803307 @default.
- W2154256357 cites W2065703980 @default.
- W2154256357 cites W2065784518 @default.
- W2154256357 cites W2070759851 @default.
- W2154256357 cites W2072959389 @default.
- W2154256357 cites W2079268496 @default.
- W2154256357 cites W2079784249 @default.
- W2154256357 cites W2081885998 @default.
- W2154256357 cites W2082507486 @default.
- W2154256357 cites W2082826197 @default.
- W2154256357 cites W2084087532 @default.
- W2154256357 cites W2085585854 @default.
- W2154256357 cites W2086210544 @default.
- W2154256357 cites W2088552509 @default.
- W2154256357 cites W2089340540 @default.
- W2154256357 cites W2090789862 @default.
- W2154256357 cites W2093359890 @default.