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- W2155477306 endingPage "4052" @default.
- W2155477306 startingPage "4041" @default.
- W2155477306 abstract "Abstract Hemophagocytic lymphohistiocytosis (HLH) is a syndrome of pathologic immune activation, occurring as either a familial disorder or a sporadic condition, in association with a variety of triggers. This immune dysregulatory disorder is prominently associated with cytopenias and a unique combination of clinical signs and symptoms of extreme inflammation. Prompt initiation of immunochemotherapy is essential for survival, but timely diagnosis may be challenging because of the rarity of HLH, its variable presentation, and the time required to perform diagnostic testing. Therapy is complicated by dynamic clinical course, high risk of treatment-related morbidity, and disease recurrence. Here, we review the clinical manifestations and patterns of HLH and describe our approach to the diagnosis and therapy for this elusive and potentially lethal condition." @default.
- W2155477306 created "2016-06-24" @default.
- W2155477306 creator A5006499960 @default.
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- W2155477306 creator A5048012532 @default.
- W2155477306 creator A5048379987 @default.
- W2155477306 creator A5068698149 @default.
- W2155477306 date "2011-10-13" @default.
- W2155477306 modified "2023-10-11" @default.
- W2155477306 title "How I treat hemophagocytic lymphohistiocytosis" @default.
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