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- W2158884830 abstract "Retroperitoneal fibrosis encompasses a range of diseases characterized by the presence of a fibro-inflammatory tissue, which usually surrounds the abdominal aorta, iliac arteries and extends into the retroperitoneum to envelop neighboring structures such as the ureters.We present two cases with multisystem disease involving retroperitoneal fibrosis, renal failure, pulmonary infiltrates and skeletal abnormalities. The unifying diagnosis of Erdheim–Chester disease (ECD) is a non-Langerhans cell histiocytosis (NLH) characterized by bilateral metaphyseal sclerosis of long bones, retroperitoneal fibrosis and multiple organ dysfunction due to the infiltrative process." @default.
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- W2158884830 date "2011-07-25" @default.
- W2158884830 modified "2023-09-25" @default.
- W2158884830 title "Unusual cases of hydronephrosis with retroperitoneal fibrosis: mystery revealed" @default.
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- W2158884830 doi "https://doi.org/10.1093/ndtplus/sfr076" @default.
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