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- W2158958878 abstract "Summary Two children with maple syrup urine disease undergoing emergency and elective surgery are reported. The administration of ketamine to a 12‐month‐old boy without neurological problems and propofol infusion to a 5‐year‐old girl with a history of convulsions, was uneventful. We believe that a, full knowledge of the pathophysiology of maple syrup urine disease and potential peri‐operative problems associated with the disease are essential, so that patients are not subjected to unnecessary risks ." @default.
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- W2158958878 date "1996-06-01" @default.
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- W2158958878 title "Anaesthetic management in maple syrup urine disease" @default.
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- W2158958878 doi "https://doi.org/10.1111/j.1365-2044.1996.tb12568.x" @default.
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