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- W2218640529 abstract "Erdheim-Chester hastalığı (ECD) etyolojisi bilinmeyen, multipl organ tutulumu ile seyreden, sistemik histiyositozisin nadir bir non-Langerhans formudur. Dokularda CD68 ile pozitif ve CD1a ile negatif boyanma gösteren ksantomatöz infiltrasyon ile karekterizedir. Bu makalede 62 yaşında kötü koku alma şikayeti ile başvuran ve beyin manyetik rezonans görüntüleme tetkikinde klivusta kitle ve leptomeningeal tutulum saptanan ve eşlik eden intrakardiyak kitle eksizyonu sonucu histopatolojik tanısı ECD ile uyumlu bulunan bir olgu bildirilmektedir. Olgunun sıra dışı belirtileri, histopatolojik ve radyodiagnostik bulguları eşliğinde sunulmakta ve bu nadir hastalığın ayırıcı tanısı tartışılmaktadır." @default.
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- W2218640529 date "2015-09-01" @default.
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- W2218640529 title "Kalp ve beyin tutulumlu Erdheim-Chester hastalığı" @default.
- W2218640529 doi "https://doi.org/10.19161/etd.344134" @default.
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