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- W2228037482 abstract "Les facteurs de transcriptions Signal Transducer and Activator Transcription (STAT) sont essentiels pour la regulation de genes impliques dans plusieurs fonctions biologiques, y compris la reponse immunitaire. Nous avons etudie un patient ayant une nouvelle mutation ponctuelle heterozygote dans le gene STAT5B. Les symptomes cliniques majeurs observes chez ce patient sont thrombocytopenie immune (TPI), lymphadenopathies, concentration elevee en anticorps IgM dans le serum et hypergammaglobulinemie. Nous avons observe une accumulation anormale de lymphocytes T memoires effecteurs (LME). Une analyse du transcriptome du patient a permis d'observer une sous-expression des genes regules par STAT5. De plus, nous avons revele que les LME du patient etaient resistants a la mort induite par la restimulation du TCR. Ces resultats demontrent un role important et inattendu de STAT5 dans la regulation de l'homeostasie des lymphocytes T memoires pendant la restimulation du TCR." @default.
- W2228037482 created "2016-06-24" @default.
- W2228037482 creator A5044690368 @default.
- W2228037482 date "2015-01-01" @default.
- W2228037482 modified "2023-09-24" @default.
- W2228037482 title "Regulation of CD4⁺ memory T cell homeostasis by STAT5 during TCR restimulation" @default.
- W2228037482 hasPublicationYear "2015" @default.
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