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- W2284553164 abstract "Medulloblastoma is the most common malignant brain tumor in children and can be divided in different molecular subgroups. Patients whose tumor is classified as a Group 3 tumor have a dismal prognosis. However only very few tumor models are available for this subgroup.We established a robust orthotopic xenograft model with a cell line derived from the malignant pleural effusions of a child suffering from a Group 3 medulloblastoma.Besides classical characteristics of this tumor subgroup, the cells display cancer stem cell characteristics including neurosphere formation, multilineage differentiation, CD133/CD15 expression, high ALDH-activity and high tumorigenicity in immunocompromised mice with xenografts exactly recapitulating the original tumor architecture.This model using unmanipulated, human medulloblastoma cells will enable translational research, specifically focused on Group 3 medulloblastoma." @default.
- W2284553164 created "2016-06-24" @default.
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- W2284553164 date "2016-02-17" @default.
- W2284553164 modified "2023-09-27" @default.
- W2284553164 title "MB3W1 is an orthotopic xenograft model for anaplastic medulloblastoma displaying cancer stem cell- and Group 3-properties" @default.
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- W2284553164 doi "https://doi.org/10.1186/s12885-016-2170-z" @default.
- W2284553164 hasPubMedCentralId "https://www.ncbi.nlm.nih.gov/pmc/articles/4756501" @default.
- W2284553164 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/26883117" @default.
- W2284553164 hasPublicationYear "2016" @default.
- W2284553164 type Work @default.