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- W2312397441 abstract "症例, 65歳,男性.主訴,浮腫,めまい,倦怠感末梢神経および自律神経障害,ネフローゼ症候群,心肥大,肝腫大を認め,胃生検,神経生検より原発性アミロイドーシスと診断した.血清免疫グロブリンは低値であったが, PHAおよびCon Aにたいするリンパ球の反応性は低下し,表面マーカーの検索にて, OKT 8の減少, OKT 4の増加, OKT 4/OKT 8比の増加(3.56)を認めた. DMSOの投与を行ったが,心停止のために死亡した.剖検上,肝,心,腎など全身にアミロイドの沈着があり,その生化学的分析の結果,分子量10Kdを主体とするAL (λ)型のアミロイド蛋白を同定した.家族性アミロイドーシスでは神経障害は高頻度かつ重篤である.本例は原発性であるにもかかわらず多彩な神経症状を示し,興味ある症例と考えられたので報告した." @default.
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- W2312397441 date "1989-01-01" @default.
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- W2312397441 title "A autopsy case of primary non-familial amyloidosis with remarkable neuropathy. Immunopathological aspect of AL amyloid protein." @default.
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- W2312397441 doi "https://doi.org/10.2177/jsci.12.245" @default.
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