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- W2314973792 abstract "無症候性原発性胆汁性肝硬変症として経過観察中に門脈体循環シャントによる肝性脳症を呈した1例を経験したので報告する.症例は62歳の女性で,6年前当科に入院し無症候性原発性胆汁性肝硬変症と診断,以後外来で経過観察していた.約2年前より言語と動作が緩慢になり,また血中アンモニア値が時々上昇するため再入院した.腹部血管造影で,奇静脈および傍臍静脈を介するシャントが確認され,主症状はこれら門脈体循環シャントによる肝性脳症であることが明らかになった.他の症状,一般臨床検査所見,腹腔鏡所見についてはこの6年間においてほとんど変化はみられなかった.ただ,肝生検組織所見で門脈枝の潰れが最近より顕著となった.原発性胆汁性肝硬変では,しばしば門脈圧亢進を伴うが,非硬変期からこのような脳症をおこすことは稀であり,本疾患の成因および臨床像を考えるうえで参考になる症例と考え報告した." @default.
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- W2314973792 date "1989-01-01" @default.
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- W2314973792 title "A case of primary biliary cirrhosis at the precirrhotic stage which developed hepatic encephalopathy caused by a porto-systemic shunt." @default.
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