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- W2317338631 abstract "Short QT syndrome is a rare inherited autosomal dominant cardiac channelopathy associated with malignant ventricular and atrial arrhythmias. A shortened corrected QT interval is a marker for risk of malignant arrhythmias, which are secondary to increased transmural dispersion of repolarization. The underlying gain of function mutations in the potassium channels are most common but genetic testing remains low yield. This review discusses the cellular mechanisms, genetic involvement, clinical presentation, and current recommended management of patients with short QT syndrome relevant to current clinical practice." @default.
- W2317338631 created "2016-06-24" @default.
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- W2317338631 date "2016-07-01" @default.
- W2317338631 modified "2023-10-18" @default.
- W2317338631 title "Short QT Syndrome in Current Clinical Practice" @default.
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- W2317338631 doi "https://doi.org/10.1097/crd.0000000000000091" @default.
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