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- W2317455005 abstract "Pyroglobulinemiaを伴うIgD-λ型骨髄腫の希有な1症例を報告する.患者は70才,男性.腰痛と大量の下血を主訴に入院となつた.検索の結果,直腸S状結腸の非特異的びまん性出血性炎症像に加え,汎血球減少,血沈高度亢進,骨のPmched out lesion, IgD-λ型M蛋白血症,骨髄の著明な骨髄腫細胞の増殖などが認められ,多発性骨髄腫と診断した.本例の大量の下血には,腰痛時に頻用していたindomethacin坐薬の直接作用に加え,血小板減少および, M蛋白による血小板機能低下,凝固因子活性低下.線溶亢進などの関与が示唆された.血清非働化時発見されたpyroglobulinはIgDによるものであることが判明した.その熱凝固性,酸ゲル化反応は非常に緩和ではあるが, glycine, urea, guanidineなどにて熱凝固性が消失または抑制されることより,従来から報告されている定型的なIgG型pyroglobulinと類似の熱凝固化機序が示唆された." @default.
- W2317455005 created "2016-06-24" @default.
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- W2317455005 date "1984-01-01" @default.
- W2317455005 modified "2023-10-05" @default.
- W2317455005 title "A case of IgD-.LAMBDA. type multiple myeloma with pyroglobulinemia." @default.
- W2317455005 doi "https://doi.org/10.2169/naika.73.980" @default.
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