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- W2319653012 abstract "von Hippel-Lindau病(以下,VHL病と略記)は遺伝性多発腫瘍性症候群で,膵病変も高率に合併する.VHL病に合併した膵病変に対し,膵頭十二指腸切除術と膵尾部切除術を同時に施行した2例を経験した.症例1は33歳,男性.膵鉤部,膵尾部ならびに両側副腎に腫瘍性病変を認め,膵頭十二指腸切除術,膵尾部切除術ならびに両側副腎摘出術を施行した.膵鉤部病変は神経内分泌腫瘍,膵尾部病変は漿液性嚢胞であった.遺伝子検査でVHL病と診断された.術後に膵瘻(ISGPF Grade B)を認めた.症例2は60歳,女性.症例1の母親.膵頭部と膵尾部に腫瘍性病変を指摘された.VHL病と診断され,膵頭十二指腸切除術ならびに膵尾部切除術を施行した.膵鉤部病変は神経内分泌腫瘍,膵鉤部病変は漿液性嚢胞腺腫であった.術後に膵瘻(ISGPF Grade B)を認めた." @default.
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- W2319653012 date "2013-01-01" @default.
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- W2319653012 title "Middle-preserving Pancreatectomy for Multicentric Pancreatic Lesions in 2 Cases with von Hippel-Lindau Disease" @default.
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- W2319653012 doi "https://doi.org/10.3919/jjsa.74.1366" @default.
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