Matches in SemOpenAlex for { <https://semopenalex.org/work/W2319934108> ?p ?o ?g. }
Showing items 1 to 52 of
52
with 100 items per page.
- W2319934108 endingPage "248" @default.
- W2319934108 startingPage "247" @default.
- W2319934108 abstract "Treacher Collins syndrome, also known as mandibulofacial dysostosis, is an autosomal dominant disorder of the cranio-facial morphogenesis affecting 1 of 50,000 live newborns. Most children with this disease present with bilateral, severe conductive hearing loss due to bilateral aural atresia. Auditory rehabilitation of these children can be effectively carried out with bone-anchored hearing aids (Baha). The aim of this retrospective study is to review the “Bambino Gesù” Children's Hospital's experience with Baha in Treacher Collins patients, highlighting the tips and pitfalls of Baha surgery in this particular population.The clinical charts were reviewed of all children with a Treacher Collins syndrome diagnosis receiving a Baha in the “Bambino Gesù” Children's Hospital from January 1995 to January 2010. Data were collected concerning patients’ anagraphics and medical history, comorbidities, surgical technique, complications and functional outcome.23 Treacher Collins children were included. A two-stage surgery was adopted in 51% (n = 12) cases, while a one-stage approach was chosen in 49% (n = 11). 2 children underwent 1st stage surgery as they were younger than 5. There were neither cases of osseointegration failure, nor cases of traumatic implant loss. Overall, the local complication rate was not different in the one-stage and in the two-stage group. The functional gain was significantly better with the Baha than with the conventional bone-conduction hearing aids (p < 0.0002). There was no difference in terms of functional outcome between the 7 patients receiving Baha at an age younger than 5 years and the rest (p = 0.23).Baha can provide effective auditory rehabilitation for children with Treacher Collins syndrome, as long as it is performed in a tertiary care center where a multidisciplinary approach to the frequent comorbidities is possible. The main challenge of Baha surgery in this population is the poor or irregular thickness of the patient's calvarial bone, which often makes it necessary to drill additional holes, to place the fixture in contact with the dura or to use materials for bone augmentation." @default.
- W2319934108 created "2016-06-24" @default.
- W2319934108 creator A5063035669 @default.
- W2319934108 date "1994-11-01" @default.
- W2319934108 modified "2023-09-25" @default.
- W2319934108 title "The child and the environment" @default.
- W2319934108 doi "https://doi.org/10.1016/0165-5876(94)90067-1" @default.
- W2319934108 hasPublicationYear "1994" @default.
- W2319934108 type Work @default.
- W2319934108 sameAs 2319934108 @default.
- W2319934108 citedByCount "0" @default.
- W2319934108 crossrefType "journal-article" @default.
- W2319934108 hasAuthorship W2319934108A5063035669 @default.
- W2319934108 hasConcept C118552586 @default.
- W2319934108 hasConcept C141071460 @default.
- W2319934108 hasConcept C167135981 @default.
- W2319934108 hasConcept C187212893 @default.
- W2319934108 hasConcept C2779076563 @default.
- W2319934108 hasConcept C2781245598 @default.
- W2319934108 hasConcept C2908647359 @default.
- W2319934108 hasConcept C71924100 @default.
- W2319934108 hasConcept C99454951 @default.
- W2319934108 hasConceptScore W2319934108C118552586 @default.
- W2319934108 hasConceptScore W2319934108C141071460 @default.
- W2319934108 hasConceptScore W2319934108C167135981 @default.
- W2319934108 hasConceptScore W2319934108C187212893 @default.
- W2319934108 hasConceptScore W2319934108C2779076563 @default.
- W2319934108 hasConceptScore W2319934108C2781245598 @default.
- W2319934108 hasConceptScore W2319934108C2908647359 @default.
- W2319934108 hasConceptScore W2319934108C71924100 @default.
- W2319934108 hasConceptScore W2319934108C99454951 @default.
- W2319934108 hasIssue "3" @default.
- W2319934108 hasLocation W23199341081 @default.
- W2319934108 hasOpenAccess W2319934108 @default.
- W2319934108 hasPrimaryLocation W23199341081 @default.
- W2319934108 hasRelatedWork W2002120878 @default.
- W2319934108 hasRelatedWork W2003938723 @default.
- W2319934108 hasRelatedWork W2047967234 @default.
- W2319934108 hasRelatedWork W2118496982 @default.
- W2319934108 hasRelatedWork W2364998975 @default.
- W2319934108 hasRelatedWork W2369162477 @default.
- W2319934108 hasRelatedWork W2439875401 @default.
- W2319934108 hasRelatedWork W4238867864 @default.
- W2319934108 hasRelatedWork W2519357708 @default.
- W2319934108 hasRelatedWork W2525756941 @default.
- W2319934108 hasVolume "30" @default.
- W2319934108 isParatext "false" @default.
- W2319934108 isRetracted "false" @default.
- W2319934108 magId "2319934108" @default.
- W2319934108 workType "article" @default.