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- W2326079398 abstract "著明な黄疸(T-Bil. 14.3mg/dl)で入院し,入院10日目に,腹腔内出血で死亡した原発性アミロイドーシスの1剖検例(46歳男子)を報告した.黄疸は,胆石溶解の目的で,CDCAとUDCAを併用投与した2, 3日後に出現しており,黄疸出現の原因として,胆汁酸の関与が強く疑われたが,確証は得られなかった.アミロイド蛋白の分析結果から,本症例のアミロイド蛋白はAA蛋白ではなく,L鎖のfragmentがaggregateしたか,あるいはAL蛋白とは異なった他の蛋白である可能性が示唆された.死因は,肝海綿状血管腫の破裂によって,腹腔内に大量の出血が起ったことによるものであった.血管腫は,アミロイド沈着で血管壁が脆くなっていた上に,物理的圧力が加わったために破裂した,と推測された." @default.
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- W2326079398 date "1986-01-01" @default.
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- W2326079398 title "An autopsy case of primary amyloidosis associated with the development of jaundice and rupture of liver cavernous hemangioma - With reference to the results of analysis of amyloid protein." @default.
- W2326079398 doi "https://doi.org/10.2957/kanzo.27.1463" @default.
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