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- W2327432311 endingPage "210" @default.
- W2327432311 startingPage "201" @default.
- W2327432311 abstract "Since the identification of the first pathogenic mutations of mitochondrial DNA in 1988, a plethora of information about human mitochondrial diseases has been brought to light. Not surprisingly, many of these disorders affect the myocardium, because this tissue relies heavily upon oxidative metabolism. This review focuses on disorders of the respiratory chain, the only area of mammalian cellular metabolism under the control of two genomes, nuclear and mitochondrial. Consequently, defects of aerobic synthesis of adenosine triphosphate (ATP) can be due to mutations of either genome. We describe genetic mitochondrial cardiomyopathies and briefly review mouse models and the mitochondrial theory of presbycardia." @default.
- W2327432311 created "2016-06-24" @default.
- W2327432311 creator A5019742604 @default.
- W2327432311 creator A5026772758 @default.
- W2327432311 creator A5065093217 @default.
- W2327432311 date "2001-05-01" @default.
- W2327432311 modified "2023-10-12" @default.
- W2327432311 title "Mitochondria and the heart" @default.
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- W2327432311 doi "https://doi.org/10.1097/00001573-200105000-00008" @default.
- W2327432311 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/11357017" @default.
- W2327432311 hasPublicationYear "2001" @default.
- W2327432311 type Work @default.