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- W2400963559 abstract "La tumeur mixte, initialement décrite dans la parotide, est constituée d’une prolifération cellulaire épithéliale et myoépithéliale associée à un stroma remanié. Nous rapportons l’observation d’une femme hospitalisée pour un nodule sous cutané de la cuisse, d’augmentation rapide de taille en 8 mois. L’étude microscopique a montré une prolifération de cellules fusiformes, courtes, groupées ou isolées, sans atypie cyto-nucléaire ni mitose. De rares arrangements tubulaires étaient notés. Le stroma était scléro-hyalin. Les cellules tumorales exprimaient l’actine musculaire lisse, les kératines, la protéine S100 en proportion variable selon les secteurs. La plus grande partie de la tumeur avait l’aspect d’une tumeur mésenchymateuse. Le diagnostic retenu était celui d’une tumeur mixte à prédominance myoépithéliale. Cette observation illustre les difficultés de classification de ces tumeurs. Certains auteurs les considèrent comme une variante de tumeur mixte, d’autres distinguent le myoépithéliome des tumeurs mixtes, en raison de son évolution plus agressive. L’évolution rapide de notre observation tend à montrer que la prédominance de la différenciation myoépithéliale pourrait être un critère de moins bon pronostic, comme le rapportent les données de la littérature.Mixed tumor, first reported in the parotid gland, is formed from the proliferation of epithelial and myoepithelial cells in a mesenchymatous stroma. We report the case of a woman hospitalized for a subcutaneous nodule of the thigh, characterized by a fast increased in size in 8 months. Microscopic analysis showed a proliferation of grouped and isolated spindle cells, without atypia or mitotic features. Few tubular features were noted. Stroma was hyalinized or myxoid. Neoplastic cells displayed immunohistochemical positivity with smooth muscle actin, keratin and S-100 protein. This neoplasm appeared mesenchymatous. The diagnosis was mixed tumor with a predominant myoepithelial component. This case underlines the difficulties encountered in defining this neoplasm. Some authors consider that myoepithelioma is a monophasic variant of mixed tumor; others consider that myoepithelioma is different from mixed tumor because its is more agressive prognosis.The evolution of our case suggests that a myoepithelial differentiation should be a ma of poor prognosis." @default.
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- W2400963559 date "2004-06-01" @default.
- W2400963559 modified "2023-09-27" @default.
- W2400963559 title "Un nodule cutané qui évolue depuis 30 ans !" @default.
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- W2400963559 doi "https://doi.org/10.1016/s0242-6498(04)93968-5" @default.
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