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- W2410332016 abstract "Pulmonary arterial hypertension (PAH) is a severe complication of systemic sclerosis. High vascular resistance in PAH arises from an imbalance between vasodilatory mediators (prostacyclin, NO) and vasoconstrictive mediators (endothelin, thromboxane A-2). Inhaled iloprost and the dual endothelin receptor antagonist bosentan have recently been shown to be effective in controlled clinical trials. Our case report demonstrates that patients with bosentan-refractory PAH can be successfully treated with iloprost inhalation." @default.
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- W2410332016 date "2005-06-24" @default.
- W2410332016 modified "2023-09-23" @default.
- W2410332016 title "Successful therapy of bosentan-refractory pulmonary arterial hypertension (PAH) with inhalative iloprost." @default.
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