Matches in SemOpenAlex for { <https://semopenalex.org/work/W2466201214> ?p ?o ?g. }
Showing items 1 to 70 of
70
with 100 items per page.
- W2466201214 endingPage "3" @default.
- W2466201214 startingPage "152" @default.
- W2466201214 abstract "With the expansion of newborn screening to include many organic acidurias and fatty acid oxidation defects, effective therapies of these disorders will be needed. Currently severe disorders such as methylmalonic and propionic aciduria. conventional therapy with diet and oral L-camitine often prove ineffective in preventing failure to thrive and recurrent metabolic decompensations. L-carnitine provides a natural pathway for removal of the toxic metabolites in these disorders and is life saving therapy but, with poor oral absorption (25%), it is difficult to supply adequate carnitine to meet the metabolic needs of these patients. Long term intravenous L-carnitine therapy, administered through a subcutaneous venous access port in 5 patients with organic acidurias [propionic aciduria (2), methylmalonic aciduria (2), 3 methylglutaconic aciduria(1)] resulted in improved growth, lower frequency of metabolic decompensations and increased tolerance of natural protein in the diet. An added benefit was the ability to initiate fluid. electrolytes, and antibiotics during metabolic decompensations at home thus averting hospitalizations." @default.
- W2466201214 created "2016-07-22" @default.
- W2466201214 creator A5002671971 @default.
- W2466201214 creator A5028809934 @default.
- W2466201214 creator A5034930250 @default.
- W2466201214 creator A5049387021 @default.
- W2466201214 creator A5051564315 @default.
- W2466201214 creator A5079961335 @default.
- W2466201214 creator A5085991821 @default.
- W2466201214 date "1999-01-01" @default.
- W2466201214 modified "2023-09-27" @default.
- W2466201214 title "Therapy of metabolic disorders with intravenous (IV) access ports and long term intravenous L-carnitine therapy." @default.
- W2466201214 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/11400757" @default.
- W2466201214 hasPublicationYear "1999" @default.
- W2466201214 type Work @default.
- W2466201214 sameAs 2466201214 @default.
- W2466201214 citedByCount "4" @default.
- W2466201214 countsByYear W24662012142012 @default.
- W2466201214 countsByYear W24662012142014 @default.
- W2466201214 countsByYear W24662012142017 @default.
- W2466201214 crossrefType "journal-article" @default.
- W2466201214 hasAuthorship W2466201214A5002671971 @default.
- W2466201214 hasAuthorship W2466201214A5028809934 @default.
- W2466201214 hasAuthorship W2466201214A5034930250 @default.
- W2466201214 hasAuthorship W2466201214A5049387021 @default.
- W2466201214 hasAuthorship W2466201214A5051564315 @default.
- W2466201214 hasAuthorship W2466201214A5079961335 @default.
- W2466201214 hasAuthorship W2466201214A5085991821 @default.
- W2466201214 hasConcept C126322002 @default.
- W2466201214 hasConcept C2776917539 @default.
- W2466201214 hasConcept C2777090595 @default.
- W2466201214 hasConcept C2778159418 @default.
- W2466201214 hasConcept C2778435403 @default.
- W2466201214 hasConcept C2779488543 @default.
- W2466201214 hasConcept C2779821038 @default.
- W2466201214 hasConcept C2781099255 @default.
- W2466201214 hasConcept C2910256814 @default.
- W2466201214 hasConcept C71924100 @default.
- W2466201214 hasConcept C90924648 @default.
- W2466201214 hasConceptScore W2466201214C126322002 @default.
- W2466201214 hasConceptScore W2466201214C2776917539 @default.
- W2466201214 hasConceptScore W2466201214C2777090595 @default.
- W2466201214 hasConceptScore W2466201214C2778159418 @default.
- W2466201214 hasConceptScore W2466201214C2778435403 @default.
- W2466201214 hasConceptScore W2466201214C2779488543 @default.
- W2466201214 hasConceptScore W2466201214C2779821038 @default.
- W2466201214 hasConceptScore W2466201214C2781099255 @default.
- W2466201214 hasConceptScore W2466201214C2910256814 @default.
- W2466201214 hasConceptScore W2466201214C71924100 @default.
- W2466201214 hasConceptScore W2466201214C90924648 @default.
- W2466201214 hasLocation W24662012141 @default.
- W2466201214 hasOpenAccess W2466201214 @default.
- W2466201214 hasPrimaryLocation W24662012141 @default.
- W2466201214 hasRelatedWork W1808424459 @default.
- W2466201214 hasRelatedWork W2057720371 @default.
- W2466201214 hasRelatedWork W2069791434 @default.
- W2466201214 hasRelatedWork W2085986436 @default.
- W2466201214 hasRelatedWork W2365649558 @default.
- W2466201214 hasRelatedWork W2466201214 @default.
- W2466201214 hasRelatedWork W2983947450 @default.
- W2466201214 hasRelatedWork W3016778534 @default.
- W2466201214 hasRelatedWork W3160268945 @default.
- W2466201214 hasRelatedWork W1857864242 @default.
- W2466201214 hasVolume "30 Suppl 2" @default.
- W2466201214 isParatext "false" @default.
- W2466201214 isRetracted "false" @default.
- W2466201214 magId "2466201214" @default.
- W2466201214 workType "article" @default.