FRINK Linked Data Fragments server

Matches in SemOpenAlex for { <https://semopenalex.org/work/W2472721807> ?p ?o ?g. }

• W2472721807 endingPage "276" @default.
• W2472721807 startingPage "275" @default.
• W2472721807 abstract "Letters to the EditorMaffucci's Syndrome Christine Hoeffel, MD Jean-Claude Hoeffel, and MD Rajae KadiriMD Christine Hoeffel Hôpital Jeanne d' Arc, B.P. 301, 54201 Toul Cedex, France Search for more papers by this author , Jean-Claude Hoeffel Hôpital Jeanne d' Arc, B.P. 301, 54201 Toul Cedex, France Search for more papers by this author , and Rajae Kadiri Department of Radiology, CHU Ibn Rashid, Casablanca, Morocco Search for more papers by this author Published Online:1 May 1998https://doi.org/10.5144/0256-4947.1998.275SectionsPDF ToolsAdd to favoritesDownload citationTrack citations ShareShare onFacebookTwitterLinked InRedditEmail AboutIntroductionTo the Editor. We have read with interest the recent case report of Desai et al., on Maffucci's syndrome.1 We have also encountered a similar case with huge soft tissue abnormalities but proportionate to the osseous lesions of the leg and foot (Figures 1 and 2). References of the literature regarding Maffucci's syndrome should include references nos. 2-5, and also that of Mirra et al.,6 which shows a nice image of Maffucci's syndrome.Figure 1. Large osseous lesions of left distal and proximal tibia and fibula with calcifications.Download FigureFigure 2. Huge soft tissue masses of toes with phleboliths.Download FigureMaffucci's syndrome represents a rare congenital long hereditary mesodermal dysplasia, manifested by multiple endochromas and soft tissue hemangiomas. Radiographic abnormalities are characteristic, consisting of typical central or eccentric radiolucent lesions containing a variable amount of calcifications and phleboliths within the affected tissue. Oilier disease may be diagnosed instead of Maffucci's syndrome until hemangiomas are discovered on physical examination. The radiographs reveal endochromas of virtually every bone, as well as soft tissue calcifications or phleboliths. The potential for both bone and soft tissue lesions to undergo sarcomatous transformation in this syndrome has been emphasized. Chondrosarcoma is the dominant malignant tumor encountered.7ARTICLE REFERENCES:1. Desai S, Kubeyinje EP, Belagavi C, Desai S. Maffucci's syndrome . Ann Saudi Med. 1997; 17: 451–3. Google Scholar2. Albregts AE, Rapini RP. Malignancy in Maffucci's syndrome . Dermatol Clin. 1995; 13: 73–8. Google Scholar3. Ben-Itzak I, Denolf FA, Amron DM, Kaplan I. The Maffucci's syndrome . J Pediatr Orthop. 1988; 8: 345–8. Google Scholar4. Kaplan RP, Wang JT, Amron DM, Kaplan L. Maffucci's syndrome: two case reports with a literature review . J Am Acad Dermatol. 1993; 29: 894–9. Google Scholar5. Lewis RJ, Ketcham AS. Maffucci's syndrome: functional and neoplastic significance . J Bone Joint Surg. 1973; 55: 1465–79. Google Scholar6. Mirra JM, Picci P, Gold RH. Bone tumors. Philadelphia: Lea and Febiger, 1989: 461–71. Google Scholar7. Sun TC, Swee RG, Shives TC, Unni KK. Chondrosarcoma in Maffucci's syndrome . J Bone Joint Surg. 1985; 67A: 1214–9. Google Scholar Previous article Next article FiguresReferencesRelatedDetails Volume 18, Issue 3May 1998 Metrics History Published online1 May 1998 InformationCopyright © 1998, Annals of Saudi MedicinePDF download" @default.
• W2472721807 created "2016-07-22" @default.
• W2472721807 creator A5072667068 @default.
• W2472721807 creator A5078826257 @default.
• W2472721807 creator A5081709796 @default.
• W2472721807 date "1998-05-01" @default.
• W2472721807 modified "2023-09-27" @default.
• W2472721807 title "Maffucci's Syndrome" @default.
• W2472721807 cites W1916178575 @default.
• W2472721807 cites W2149327209 @default.
• W2472721807 cites W2289830986 @default.
• W2472721807 cites W2313821891 @default.
• W2472721807 cites W2399833324 @default.
• W2472721807 cites W2400954355 @default.
• W2472721807 doi "https://doi.org/10.5144/0256-4947.1998.275" @default.
• W2472721807 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/17341988" @default.
• W2472721807 hasPublicationYear "1998" @default.
• W2472721807 type Work @default.
• W2472721807 sameAs 2472721807 @default.
• W2472721807 citedByCount "0" @default.
• W2472721807 crossrefType "journal-article" @default.
• W2472721807 hasAuthorship W2472721807A5072667068 @default.
• W2472721807 hasAuthorship W2472721807A5078826257 @default.
• W2472721807 hasAuthorship W2472721807A5081709796 @default.
• W2472721807 hasConcept C126838900 @default.
• W2472721807 hasConcept C136948725 @default.
• W2472721807 hasConcept C142724271 @default.
• W2472721807 hasConcept C2775894508 @default.
• W2472721807 hasConcept C2776302905 @default.
• W2472721807 hasConcept C2781266816 @default.
• W2472721807 hasConcept C71924100 @default.
• W2472721807 hasConceptScore W2472721807C126838900 @default.
• W2472721807 hasConceptScore W2472721807C136948725 @default.
• W2472721807 hasConceptScore W2472721807C142724271 @default.
• W2472721807 hasConceptScore W2472721807C2775894508 @default.
• W2472721807 hasConceptScore W2472721807C2776302905 @default.
• W2472721807 hasConceptScore W2472721807C2781266816 @default.
• W2472721807 hasConceptScore W2472721807C71924100 @default.
• W2472721807 hasIssue "3" @default.
• W2472721807 hasLocation W24727218071 @default.
• W2472721807 hasLocation W24727218072 @default.
• W2472721807 hasOpenAccess W2472721807 @default.
• W2472721807 hasPrimaryLocation W24727218071 @default.
• W2472721807 hasRelatedWork W141524600 @default.
• W2472721807 hasRelatedWork W1754602832 @default.
• W2472721807 hasRelatedWork W1841185769 @default.
• W2472721807 hasRelatedWork W2049214470 @default.
• W2472721807 hasRelatedWork W2072926321 @default.
• W2472721807 hasRelatedWork W2155887765 @default.
• W2472721807 hasRelatedWork W2317068357 @default.
• W2472721807 hasRelatedWork W2902148150 @default.
• W2472721807 hasRelatedWork W3034178005 @default.
• W2472721807 hasRelatedWork W4236339841 @default.
• W2472721807 hasVolume "18" @default.
• W2472721807 isParatext "false" @default.
• W2472721807 isRetracted "false" @default.
• W2472721807 magId "2472721807" @default.
• W2472721807 workType "article" @default.