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- W2532392004 endingPage "12" @default.
- W2532392004 startingPage "3" @default.
- W2532392004 abstract "Selective immunoglobulin A deficiency (SIgAD) is the most common primary antibody deficiency. Although more patients with SIgAD are asymptomatic, selected patients suffer from different clinical complications such as pulmonary infections, allergies, autoimmune diseases, gastrointestinal disorders and malignancy. Pathogenesis of SIgAD is still unknown; however, a defective terminal differentiation of B cells and defect in switching to IgA-producing plasma cells are presumed to be responsible. Furthermore, some cytogenic defects and monogenic mutations are associated with SIgAD. There is no specific treatment for patients with symptomatic IgA deficiency, although prophylactic antibiotic therapy along with circumstantial immunoglobulin replacement with justification and supportive care (using a product that contains minimal IgA) could be helpful for patients with a severe phenotype. The epidemiology, pathogenesis, clinical phenotype, diagnosis, prognosis, management and treatment in patients with SIgAD have been reviewed." @default.
- W2532392004 created "2016-10-28" @default.
- W2532392004 creator A5025067610 @default.
- W2532392004 creator A5040499257 @default.
- W2532392004 creator A5051258190 @default.
- W2532392004 creator A5057262090 @default.
- W2532392004 date "2017-01-01" @default.
- W2532392004 modified "2023-10-14" @default.
- W2532392004 title "Selective IgA Deficiency: Epidemiology, Pathogenesis, Clinical Phenotype, Diagnosis, Prognosis and Management" @default.
- W2532392004 cites W1277544508 @default.
- W2532392004 cites W1580506975 @default.
- W2532392004 cites W1603791930 @default.
- W2532392004 cites W1656100961 @default.
- W2532392004 cites W1696493480 @default.
- W2532392004 cites W1788262216 @default.
- W2532392004 cites W1793997246 @default.
- W2532392004 cites W1901406820 @default.
- W2532392004 cites W1966185152 @default.
- W2532392004 cites W1968885061 @default.
- W2532392004 cites W1970802795 @default.
- W2532392004 cites W1970964332 @default.
- W2532392004 cites W1977878975 @default.
- W2532392004 cites W1982858689 @default.
- W2532392004 cites W1985679029 @default.
- W2532392004 cites W1989797981 @default.
- W2532392004 cites W1990605668 @default.
- W2532392004 cites W1992061488 @default.
- W2532392004 cites W1993778625 @default.
- W2532392004 cites W1994699789 @default.
- W2532392004 cites W1994889703 @default.
- W2532392004 cites W1997426681 @default.
- W2532392004 cites W1998571601 @default.
- W2532392004 cites W1999781416 @default.
- W2532392004 cites W2002292675 @default.
- W2532392004 cites W2004215568 @default.
- W2532392004 cites W2006350616 @default.
- W2532392004 cites W2007525226 @default.
- W2532392004 cites W200767527 @default.
- W2532392004 cites W2017383716 @default.
- W2532392004 cites W2017555695 @default.
- W2532392004 cites W2018344103 @default.
- W2532392004 cites W2018691683 @default.
- W2532392004 cites W2022814769 @default.
- W2532392004 cites W2024783199 @default.
- W2532392004 cites W2025807264 @default.
- W2532392004 cites W2026228148 @default.
- W2532392004 cites W2028264954 @default.
- W2532392004 cites W2028324999 @default.
- W2532392004 cites W2034139014 @default.
- W2532392004 cites W2036350389 @default.
- W2532392004 cites W2038884795 @default.
- W2532392004 cites W2039747727 @default.
- W2532392004 cites W2041568478 @default.
- W2532392004 cites W2050254523 @default.
- W2532392004 cites W2050923622 @default.
- W2532392004 cites W2053133856 @default.
- W2532392004 cites W2054145737 @default.
- W2532392004 cites W2059758349 @default.
- W2532392004 cites W2061236157 @default.
- W2532392004 cites W2065352039 @default.
- W2532392004 cites W2066059683 @default.
- W2532392004 cites W2066738217 @default.
- W2532392004 cites W2069092871 @default.
- W2532392004 cites W2070403315 @default.
- W2532392004 cites W2073568436 @default.
- W2532392004 cites W2074318043 @default.
- W2532392004 cites W2074449231 @default.
- W2532392004 cites W2082693013 @default.
- W2532392004 cites W2085527851 @default.
- W2532392004 cites W2086614200 @default.
- W2532392004 cites W2091064926 @default.
- W2532392004 cites W2094667865 @default.
- W2532392004 cites W2099138547 @default.
- W2532392004 cites W2100456727 @default.
- W2532392004 cites W2101387673 @default.
- W2532392004 cites W2105671517 @default.
- W2532392004 cites W2107039179 @default.
- W2532392004 cites W2111137836 @default.
- W2532392004 cites W2111683145 @default.
- W2532392004 cites W2112682068 @default.
- W2532392004 cites W2113623912 @default.
- W2532392004 cites W2117403402 @default.
- W2532392004 cites W2132193209 @default.
- W2532392004 cites W2134678353 @default.
- W2532392004 cites W2135715631 @default.
- W2532392004 cites W2138854473 @default.
- W2532392004 cites W2139588786 @default.
- W2532392004 cites W2144697979 @default.
- W2532392004 cites W2146228902 @default.
- W2532392004 cites W2147929705 @default.
- W2532392004 cites W2158593444 @default.
- W2532392004 cites W2159620342 @default.
- W2532392004 cites W2160300617 @default.
- W2532392004 cites W2164678711 @default.
- W2532392004 cites W2170958757 @default.
- W2532392004 cites W2171245116 @default.
- W2532392004 cites W2235980921 @default.
- W2532392004 cites W2313774095 @default.