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- W2564304510 endingPage "795" @default.
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- W2564304510 abstract "This chapter reviews some common disorders of human craniofacial development and focuses on the clinical features and molecular basis of these varied conditions. The developmental processes that create the mature structures of the craniofacial region are dynamic, relying upon complex tissue interactions that are closely co-ordinated, both temporally and spatially. Human facial development begins at approximately four weeks post-conception and is dominated by the appearance of five processes, which surround the early oral cavity or stomodeum. Clefts involving the lip with or without the palate (CLP) or isolated clefts of the palate (CP) are some of the commonest congenital anomalies to affect the cran-iofacial region in man. Holoprosencephaly (HPE) is a clinically heterogeneous developmental field defect of the central nervous system (CNS), in which the embryonic forebrain fails to divide into distinct halves. The ectodermal dysplasias (ED) are a heterogeneous group of conditions characterised primarily by defects in the teeth, hair, nails and sweat glands." @default.
- W2564304510 created "2017-01-06" @default.
- W2564304510 creator A5062441392 @default.
- W2564304510 creator A5085747162 @default.
- W2564304510 date "2016-12-16" @default.
- W2564304510 modified "2023-10-12" @default.
- W2564304510 title "Developmental Disorders of the Craniofacial Complex" @default.
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