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- W2602534297 endingPage "704" @default.
- W2602534297 startingPage "690" @default.
- W2602534297 abstract "Objective: Pheochromocytomas and paragangliomas (PPGLs) are rare neuroendocrine tumors known to produce and secrete high levels of circulating catecholamines and their metabolites. The biochemical characteristics of these tumors can be used to divide them into three major phenotypes. The adrenergic, noradrenergic and dopaminergic phenotypes are defined by predominant elevations in epinephrine and metanephrine, norepinephrine and normetanephrine, and dopamine and 3-methoxytyramine, respectively. There are over 15 well-identified tumor-susceptibility genes responsible for approximately 40% of the cases. The objective of this review article is to outline specific genotype/biochemical phenotype relationships." @default.
- W2602534297 created "2017-04-07" @default.
- W2602534297 creator A5007685706 @default.
- W2602534297 creator A5028135050 @default.
- W2602534297 date "2017-06-01" @default.
- W2602534297 modified "2023-09-25" @default.
- W2602534297 title "Precision Medicine: An Update on Genotype/Biochemical Phenotype Relationships in Pheochromocytoma/Paraganglioma Patients" @default.
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