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- W2608314534 endingPage "443" @default.
- W2608314534 startingPage "431" @default.
- W2608314534 abstract "Introduction: Inclusion body myositis is the most common acquired muscle disease affecting older adults. It has an insidious onset with a very specific pattern of muscle involvement, but the aetiopathogenesis is still unknown. Pathologically the combination of inflammatory changes, degenerative changes as well as mitochondrial and nuclear changes are seen, and probably all contribute to the loss of muscle, however the primary abnormality remains a mystery. Treatment is currently supportive, but clinical trials are ongoing and are directed at new targets.Areas covered: Clinical profile, genetic susceptibility, pathogenesis and treatmentExpert opinion: Understanding the aetiopathogeneis is vital to identify future treatment targets. In addition, understanding the natural history and the roles of biomarkers including the anti-CN1a antibody is vital for designing future clinical trials in IBM, to be properly designed and of sufficient duration to detect clinically significant changes." @default.
- W2608314534 created "2017-05-05" @default.
- W2608314534 creator A5008704373 @default.
- W2608314534 creator A5051877073 @default.
- W2608314534 date "2017-04-26" @default.
- W2608314534 modified "2023-09-25" @default.
- W2608314534 title "Advances in inclusion body myositis: genetics, pathogenesis and clinical aspects" @default.
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