Matches in SemOpenAlex for { <https://semopenalex.org/work/W2621976172> ?p ?o ?g. }
- W2621976172 endingPage "119" @default.
- W2621976172 startingPage "110" @default.
- W2621976172 abstract "Systemic amyloidoses are complex diseases caused by the misfolding of autologous protein. Immunoglobulin light chain (AL) amyloidosis is caused by usually small plasma cell clone synthesizing light chains undergoing conformational changes that lead to their aggregation and deposition in tissues. Although the presence of heart involvement is the most important prognostic determinant, the kidney is involved in 70% of patients. Renal involvement results in significant morbidity, and renal failure limits the therapeutic options. The clinical presentation of kidney involvement is characterized by nephrotic syndrome and progressive renal failure. Diagnosis relies on the identification and accurate typing of amyloid deposits at the abdominal fat pad aspirate or with renal biopsy. Refined diagnostic and staging systems based on biomarkers have helped in assessing prognoses and evaluating responses to therapy, which has considerably improved the management of these conditions. In addition, the availability of novel, more powerful drugs targeting different steps in the pathogenic cascade of AL amyloidosis has created a favorable environment for a long-awaited improvement in the treatment of this disease." @default.
- W2621976172 created "2017-06-15" @default.
- W2621976172 creator A5080444901 @default.
- W2621976172 creator A5081387086 @default.
- W2621976172 creator A5085821633 @default.
- W2621976172 date "2017-05-01" @default.
- W2621976172 modified "2023-09-27" @default.
- W2621976172 title "Kidney Involvement in Light Chain Amyloidosis" @default.
- W2621976172 cites W1016493796 @default.
- W2621976172 cites W1567835982 @default.
- W2621976172 cites W1594036575 @default.
- W2621976172 cites W1602659283 @default.
- W2621976172 cites W175675325 @default.
- W2621976172 cites W1826218096 @default.
- W2621976172 cites W1840249871 @default.
- W2621976172 cites W1870217140 @default.
- W2621976172 cites W1963505205 @default.
- W2621976172 cites W1968646226 @default.
- W2621976172 cites W1969551915 @default.
- W2621976172 cites W1973853538 @default.
- W2621976172 cites W1976601231 @default.
- W2621976172 cites W1979458650 @default.
- W2621976172 cites W1982304467 @default.
- W2621976172 cites W1983838644 @default.
- W2621976172 cites W1984620312 @default.
- W2621976172 cites W1985462305 @default.
- W2621976172 cites W1986840808 @default.
- W2621976172 cites W1990220334 @default.
- W2621976172 cites W1994877692 @default.
- W2621976172 cites W1996638695 @default.
- W2621976172 cites W1997280623 @default.
- W2621976172 cites W1999473831 @default.
- W2621976172 cites W2001594121 @default.
- W2621976172 cites W2008384522 @default.
- W2621976172 cites W2009947511 @default.
- W2621976172 cites W2012580507 @default.
- W2621976172 cites W2012680794 @default.
- W2621976172 cites W2017612047 @default.
- W2621976172 cites W2018928569 @default.
- W2621976172 cites W2020985325 @default.
- W2621976172 cites W2022856048 @default.
- W2621976172 cites W2022862731 @default.
- W2621976172 cites W2024639218 @default.
- W2621976172 cites W2027076242 @default.
- W2621976172 cites W2030131482 @default.
- W2621976172 cites W2037825770 @default.
- W2621976172 cites W2042657558 @default.
- W2621976172 cites W2054721388 @default.
- W2621976172 cites W2058789242 @default.
- W2621976172 cites W2061028095 @default.
- W2621976172 cites W2063772107 @default.
- W2621976172 cites W2063939741 @default.
- W2621976172 cites W2070335603 @default.
- W2621976172 cites W2077918440 @default.
- W2621976172 cites W2082937378 @default.
- W2621976172 cites W2092074428 @default.
- W2621976172 cites W2098093182 @default.
- W2621976172 cites W2104654583 @default.
- W2621976172 cites W2106411455 @default.
- W2621976172 cites W2106512137 @default.
- W2621976172 cites W2107403553 @default.
- W2621976172 cites W2107985278 @default.
- W2621976172 cites W2108020531 @default.
- W2621976172 cites W2109651910 @default.
- W2621976172 cites W2109740502 @default.
- W2621976172 cites W2110096325 @default.
- W2621976172 cites W2111080788 @default.
- W2621976172 cites W2118848299 @default.
- W2621976172 cites W2128536827 @default.
- W2621976172 cites W2128583637 @default.
- W2621976172 cites W2133838188 @default.
- W2621976172 cites W2135482314 @default.
- W2621976172 cites W2137477100 @default.
- W2621976172 cites W2143496573 @default.
- W2621976172 cites W2144086680 @default.
- W2621976172 cites W2147055495 @default.
- W2621976172 cites W2147289989 @default.
- W2621976172 cites W2151953595 @default.
- W2621976172 cites W2161231801 @default.
- W2621976172 cites W2161648900 @default.
- W2621976172 cites W2162210749 @default.
- W2621976172 cites W2171033052 @default.
- W2621976172 cites W2171552949 @default.
- W2621976172 cites W2184306448 @default.
- W2621976172 cites W2257690238 @default.
- W2621976172 cites W2270408688 @default.
- W2621976172 cites W2270960065 @default.
- W2621976172 cites W2282508430 @default.
- W2621976172 cites W2330120407 @default.
- W2621976172 cites W2414653379 @default.
- W2621976172 cites W2509638489 @default.
- W2621976172 cites W2511585546 @default.
- W2621976172 cites W2530902406 @default.
- W2621976172 cites W2550424027 @default.
- W2621976172 cites W2555124885 @default.
- W2621976172 cites W2558649598 @default.
- W2621976172 cites W2582406722 @default.
- W2621976172 cites W2597447225 @default.