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- W2670875745 abstract "Les thromboses veineuses au cours de la maladie cœliaque sont signalées dans la littérature, surtout chez l’adulte. Des facteurs de risque thrombophiliques ont été identifiés. Nous rapportons deux observations.Premier cas : patiente âgée de 63 ans hospitalisée pour thrombose veineuse cérébrale sur maladie cœliaque. Le bilan a révélé une hyperhomocystéinémie et des antiphospholipides de type β2GPI. Second cas : patiente de 19 ans admise pour troubles de la conscience en rapport avec une thrombose du sinus longitudinal. Le bilan retrouve un déficit en protéine S ; l’examen anatomopathologique des biopsies jéjunales conclut à une atrophie villositaire ; les anticorps antiendomysium et antigliadine sont positifs. Sous anticoagulants, l’évolution est favorable dans les deux cas.Si les thromboses veineuses associées à la maladie cœliaque sont de siège insolite, la localisation cérébrale reste exceptionnelle. La recherche de facteurs de risque est indispensable chez ces patients. Le régime sans gluten reste le traitement essentiel de la maladie cœliaque.Thrombosis events may occur in celiac disease. Thrombophilic risk factors have been reported.To report two cases of cerebral venous thrombosis in celiac disease patients and to determine associated thrombophilic factors. Case 1: a 63-year-old woman was admitted for cerebral venous thrombosis. Her past history included celiac disease which was untreated for the last 10 years. Biological data showed moderate hyperhomocysteinemia and positive reaction for antiphospholipid antibodies. Case 2: a 19-year-old girl was hospitalized for seizures and impaired consciousness. MRA demonstrated longitudinal sinus thrombosis with parietal infarction. Biological findings showed: protein S deficiency and positive reaction for antiendomysium and antigliadin antibodies. Gastroesophageal endoscopy with biopsy showed villous atrophy. Both patients improved under anticoagulant treatment.The sites of associated venous thrombosis are generally unusual in celiac disease, yet the cerebral localization is only exceptionally reported. It is essential to search for risk factors. Gluten-free diet remains the mainstay treatment for patients with celiac disease." @default.
- W2670875745 created "2017-06-30" @default.
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- W2670875745 date "2012-06-01" @default.
- W2670875745 modified "2023-10-17" @default.
- W2670875745 title "Association maladie cœliaque et thrombose veineuse cérébrale. Revue de deux observations" @default.
- W2670875745 doi "https://doi.org/10.1016/j.revmed.2012.03.160" @default.
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